Diagnosis Code

D67 HEREDITARY FACTOR IX DEFICIENCY


Code Information

Diagnosis Code: D67

Short Description: Hereditary factor IX deficiency

Long Description: Hereditary factor IX deficiency

The code D67 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
      • Hereditary factor IX deficiency (D67)
        • D67 Hereditary factor IX deficiency

Code Version: 2022 ICD-10-CM


Synonyms

  • Congenital factor IX deficiency variant
  • Congenital factor IX deficiency with inhibitor
  • Congenital factor IX deficiency without inhibitor
  • Factor IX deficiency
  • Hereditary factor IX deficiency disease
  • Hereditary factor IX deficiency disease with inhibitor
  • Hereditary factor IX deficiency disease without inhibitor
  • Mild hereditary factor IX deficiency disease with inhibitor
  • Mild hereditary factor IX deficiency disease without inhibitor
  • Moderate hereditary factor IX deficiency disease with inhibitor
  • Moderate hereditary factor IX deficiency disease without inhibitor
  • Severe hereditary factor IX deficiency disease with inhibitor
  • Severe hereditary factor IX deficiency disease without inhibitor

References to Index of Diseases and Injuries

The code D67 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Christmas disease
    • Factor IX deficiency (with functional defect)
    • Hemophilia B
    • Plasma thromboplastin component [PTC] deficiency

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D67 Right Arrow 286.1 Cong factor IX disorder

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description


This page was last updated on: 10/1/2023