Diagnosis Code: D70.0

Short Description: Congenital agranulocytosis

Long Description: Congenital agranulocytosis

The code D70.0 is VALID for claim submission

Code Classification:

• Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
  • Other disorders of blood and blood-forming organs (D70-D77)
    • Neutropenia (D70)
      • D70.0 Congenital agranulocytosis

Code Version: 2022 ICD-10-CM

Synonyms

• Autosomal dominant severe congenital neutropenia
• Autosomal recessive severe congenital neutropenia due to CSF3R deficiency
• Autosomal recessive severe congenital neutropenia due to CXCR2 deficiency
• Autosomal recessive severe congenital neutropenia due to G6PC3 deficiency
• Autosomal recessive severe congenital neutropenia due to JAGN1 deficiency
• Complete deafness
• Congenital deafness
• Congenital dyserythropoietic anemia
• Congenital neutropenia
• Congenital neutropenia, myelofibrosis, nephromegaly syndrome
• Giant platelet syndrome
• Kostmann syndrome
• Myelofibrosis
• Neutropenia, monocytopenia, deafness syndrome
• Onycho-tricho-dysplasia neutropenia syndrome
• Periodontitis due to congenital neutropenia
• Periodontitis due to infantile genetic agranulocytosis
• Trichothiodystrophy
• X-linked dyserythropoietic anemia with abnormal platelets and neutropenia
• X-linked severe congenital neutropenia

Diagnostic Related Group(s)

The code D70.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)

• Major Hematological And Immunological Diagnoses Except Sickle Cell Crisis And Coagulation Disorders With Mcc (808)
• Major Hematological And Immunological Diagnoses Except Sickle Cell Crisis And Coagulation Disorders With Cc (809)
• Major Hematological And Immunological Diagnoses Except Sickle Cell Crisis And Coagulation Disorders Without Cc/mcc (810)

References to Index of Diseases and Injuries

The code D70.0 has the following ICD-10-CM references to the Index of Diseases and Injuries

• Inclusion Terms:
  • Congenital neutropenia
  • Infantile genetic agranulocytosis
  • Kostmann's disease

Crosswalk Information

Similar Codes

This page was last updated on: 10/1/2023

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