Diagnosis Code: D76.1

Short Description: Hemophagocytic lymphohistiocytosis

Long Description: Hemophagocytic lymphohistiocytosis

The code D76.1 is VALID for claim submission

Code Classification:

• Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
  • Other disorders of blood and blood-forming organs (D70-D77)
    • Oth dis with lymphoreticular and reticulohistiocytic tissue (D76)
      • D76.1 Hemophagocytic lymphohistiocytosis

Code Version: 2022 ICD-10-CM

Synonyms

• Acquired hemophagocytic lymphohistiocytosis associated with malignant disease
• Familial hemophagocytic lymphohistiocytosis
• Hemolytic erythrophagocytic syndrome
• Hemolytic erythrophagocytic syndrome
• Hemolytic erythrophagocytic syndrome
• Hemolytic erythrophagocytic syndrome
• Hemolytic erythrophagocytic syndrome
• Hemolytic erythrophagocytic syndrome
• Hemophagocytic lymphohistiocytosis
• Hemophagocytic lymphohistiocytosis
• Hemophagocytic lymphohistiocytosis
• Lipochrome histiocytosis - familial
• Macrophage activation syndrome
• Macrophage activation syndrome
• Macrophage activation syndrome due to juvenile systemic onset arthritis
• Malignant white blood cell disorder
• Secondary hemophagocytic lymphohistiocytosis
• Secondary hemophagocytic lymphohistiocytosis

Diagnostic Related Group(s)

The code D76.1 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)

• Reticuloendothelial And Immunity Disorders With Mcc (814)
• Reticuloendothelial And Immunity Disorders With Cc (815)
• Reticuloendothelial And Immunity Disorders Without Cc/mcc (816)

References to Index of Diseases and Injuries

The code D76.1 has the following ICD-10-CM references to the Index of Diseases and Injuries

• Inclusion Terms:
  • Familial hemophagocytic reticulosis
  • Histiocytoses of mononuclear phagocytes

Crosswalk Information

Similar Codes

This page was last updated on: 10/1/2023

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