Diagnosis Code

E70.321 TYROSINASE POSITIVE OCULOCUTANEOUS ALBINISM


Code Information

Diagnosis Code: E70.321

Short Description: Tyrosinase positive oculocutaneous albinism

Long Description: Tyrosinase positive oculocutaneous albinism

The code E70.321 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Disorders of aromatic amino-acid metabolism (E70)
        • E70.321 Tyrosinase positive oculocutaneous albinism

Code Version: 2022 ICD-10-CM


Synonyms

  • Brown oculocutaneous albinism
  • Rufous albinism
  • Tyrosinase-positive oculocutaneous albinism

References to Index of Diseases and Injuries

The code E70.321 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Albinism II
    • Oculocutaneous albinism ty-pos

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E70.321 Right Arrow 270.2 Arom amin-acid metab NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E70 Disorders of aromatic amino-acid metabolism
E70.0 Classical phenylketonuria
E70.1 Other hyperphenylalaninemias
E70.2 Disorders of tyrosine metabolism
E70.20 Disorder of tyrosine metabolism, unspecified
E70.21 Tyrosinemia
E70.29 Other disorders of tyrosine metabolism
E70.3 Albinism
E70.30 Albinism, unspecified
E70.31 Ocular albinism
E70.310 X-linked ocular albinism
E70.311 Autosomal recessive ocular albinism
E70.318 Other ocular albinism
E70.319 Ocular albinism, unspecified
E70.32 Oculocutaneous albinism
E70.320 Tyrosinase negative oculocutaneous albinism
E70.328 Other oculocutaneous albinism
E70.329 Oculocutaneous albinism, unspecified
E70.33 Albinism with hematologic abnormality
E70.330 Chediak-Higashi syndrome
E70.331 Hermansky-Pudlak syndrome
E70.338 Other albinism with hematologic abnormality
E70.339 Albinism with hematologic abnormality, unspecified
E70.39 Other specified albinism
E70.4 Disorders of histidine metabolism
E70.40 Disorders of histidine metabolism, unspecified
E70.41 Histidinemia
E70.49 Other disorders of histidine metabolism
E70.5 Disorders of tryptophan metabolism
E70.8 Other disorders of aromatic amino-acid metabolism
E70.81 Aromatic L-amino acid decarboxylase deficiency
E70.89 Other disorders of aromatic amino-acid metabolism
E70.9 Disorder of aromatic amino-acid metabolism, unspecified


This page was last updated on: 10/1/2023