Diagnosis Code

Q04.9 CONGENITAL MALFORMATION OF BRAIN, UNSPECIFIED


Code Information

Diagnosis Code: Q04.9

Short Description: Congenital malformation of brain, unspecified

Long Description: Congenital malformation of brain, unspecified

The code Q04.9 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of the nervous system (Q00-Q07)
      • Other congenital malformations of brain (Q04)
        • Q04.9 Congenital malformation of brain, unspecified

Code Version: 2022 ICD-10-CM


Synonyms

  • Anomalies of cerebellum
  • Aplasia cutis congenita secondary to malformation syndrome
  • Bilateral renal hypoplasia
  • Brain malformation, congenital heart disease, postaxial polydactyly syndrome
  • Brain malformations, musculoskeletal abnormalities, facial dysmorphism, intellectual disability syndrome
  • BRESEK syndrome
  • Cerebellar cortical dysplasia
  • Cerebro-costo-mandibular syndrome
  • Cerebrofacioarticular syndrome
  • Choreoathetosis
  • CODAS syndrome
  • Combined malformation of central nervous system and skeletal muscle
  • Congenital anomaly of brain
  • Congenital anomaly of cerebrum
  • Congenital atresia of duodenum
  • Congenital brain damage
  • Congenital corneal dystrophy
  • Congenital hypotrichia
  • Congenital labioscrotal agenesis, cerebellar malformation, corneal dystrophy, facial dysmorphism syndrome
  • Congenital muscular hypertrophy-cerebral syndrome
  • Diplegia
  • Disorder of ornithine metabolism
  • Dysplasia with defective mineralization
  • Early-onset epilepsy, intellectual disability, brain anomalies syndrome
  • Endocrine-cerebro-osteodysplasia syndrome
  • Epilepsy due to congenital anomaly of brain
  • Familial visceral neuropathy
  • Focal epilepsy, intellectual disability, cerebro-cerebellar malformation syndrome
  • Global developmental delay, alopecia, macrocephaly, facial dysmorphism, structural brain anomalies syndrome
  • Hypernatremia
  • Intellectual disability, obesity, brain malformation, facial dysmorphism syndrome
  • Left renal hypoplasia
  • Lethal brain and heart developmental defects syndrome
  • Lethal fetal brain malformation, duodenal atresia, bilateral renal hypoplasia syndrome
  • Leukoencephalopathy, thalamus and brainstem anomalies, high lactate syndrome
  • Linear hypopigmentation and craniofacial asymmetry with acral, ocular and brain anomalies
  • Microcephalus, brain defect, spasticity, hypernatremia syndrome
  • Microphthalmia with brain and digit anomaly
  • Microphthalmos due to Delleman syndrome
  • Mitochondrial DNA depletion syndrome hepatocerebrorenal form
  • Multiple brain anomalies
  • Muscle eye brain disease with bilateral multicystic leukodystrophy
  • Oculocerebrocutaneous syndrome
  • Oculocerebrodental syndrome
  • Oculopalatocerebral syndrome
  • Persistent hyperplastic primary vitreous
  • Right renal hypoplasia
  • Severe oculo-renal-cerebellar syndrome
  • Spastic diplegia
  • Spastic paralysis
  • Visceral neuropathy and brain anomaly with facial dysmorphism and developmental delay syndrome
  • X-linked cerebral, cerebellar, coloboma syndrome

References to Index of Diseases and Injuries

The code Q04.9 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Congenital anomaly NOS of brain
    • Congenital deformity NOS of brain
    • Congenital disease or lesion NOS of brain
    • Multiple anomalies NOS of brain, congenital

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q04.9 Right Arrow 742.9 Nervous system anom NOS

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q04 Other congenital malformations of brain
Q04.0 Congenital malformations of corpus callosum
Q04.1 Arhinencephaly
Q04.2 Holoprosencephaly
Q04.3 Other reduction deformities of brain
Q04.4 Septo-optic dysplasia of brain
Q04.5 Megalencephaly
Q04.6 Congenital cerebral cysts
Q04.8 Other specified congenital malformations of brain


This page was last updated on: 10/1/2023