Diagnosis Code

Q25.47 RIGHT AORTIC ARCH


Code Information

Diagnosis Code: Q25.47

Short Description: Right aortic arch

Long Description: Right aortic arch

The code Q25.47 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of the circulatory system (Q20-Q28)
      • Congenital malformations of great arteries (Q25)
        • Q25.47 Right aortic arch

Code Version: 2022 ICD-10-CM


Synonyms

  • Congenital abnormality of thoracic aorta and pulmonary arteries
  • Congenital absence of left pulmonary artery
  • Congenital anomaly of aortic arch AND/OR descending aorta
  • Dextrotransposition of aorta
  • Right aortic arch
  • Right aortic arch branching pattern
  • Vascular ring with right aortic arch
  • Vascular ring with right aortic arch and left arterial duct from anomalous retroesophageal brachiocephalic artery
  • Vascular ring with right aortic arch and right arterial ligament with absent left pulmonary artery

Diagnostic Related Group(s)

The code Q25.47 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Cardiac Congenital And Valvular Disorders With Mcc (306)
  • Cardiac Congenital And Valvular Disorders Without Mcc (307)

References to Index of Diseases and Injuries

The code Q25.47 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Persistent right aortic arch

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q25.47 Right Arrow 747.21 Anomalies of aortic arch

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q25 Congenital malformations of great arteries
Q25.0 Patent ductus arteriosus
Q25.1 Coarctation of aorta
Q25.2 Atresia of aorta
Q25.21 Interruption of aortic arch
Q25.29 Other atresia of aorta
Q25.3 Supravalvular aortic stenosis
Q25.4 Other congenital malformations of aorta
Q25.40 Congenital malformation of aorta unspecified
Q25.41 Absence and aplasia of aorta
Q25.42 Hypoplasia of aorta
Q25.43 Congenital aneurysm of aorta
Q25.44 Congenital dilation of aorta
Q25.45 Double aortic arch
Q25.46 Tortuous aortic arch
Q25.48 Anomalous origin of subclavian artery
Q25.49 Other congenital malformations of aorta
Q25.5 Atresia of pulmonary artery
Q25.6 Stenosis of pulmonary artery
Q25.7 Other congenital malformations of pulmonary artery
Q25.71 Coarctation of pulmonary artery
Q25.72 Congenital pulmonary arteriovenous malformation
Q25.79 Other congenital malformations of pulmonary artery
Q25.8 Other congenital malformations of other great arteries
Q25.9 Congenital malformation of great arteries, unspecified


This page was last updated on: 10/1/2023