Diagnosis Code: Q43.1

Short Description: Hirschsprung's disease

Long Description: Hirschsprung's disease

The code Q43.1 is VALID for claim submission

Code Classification:

• Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • Other congenital malformations of the digestive system (Q38-Q45)
    • Other congenital malformations of intestine (Q43)
      • Q43.1 Hirschsprung's disease

Code Version: 2022 ICD-10-CM

Synonyms

• Aganglionosis of Auerbach's plexus
• Aganglionosis of colon
• Aganglionosis of large intestine
• Central alveolar hypoventilation syndrome
• Congenital aganglionic megacolon
• Congenital central hypoventilation
• Congenital dilatation of colon
• Congenital dilatation of colon
• Congenital dilatation of colon
• Congenital dilatation of colon
• Congenital dilatation of colon
• Extensive aganglionosis Hirschsprung disease
• Goldberg Shprintzen megacolon syndrome
• Haddad syndrome
• Hirschsprung disease of rectosigmoid region
• Hirschsprung disease with deafness and polydactyly syndrome
• Hirschsprung disease with nail hypoplasia and dysmorphism
• Hirschsprung disease with type D brachydactyly syndrome
• Hirschsprung disease, ganglioneuroblastoma syndrome
• Long segment Hirschsprung's disease
• Mowat-Wilson syndrome
• Mowat-Wilson syndrome
• Mowat-Wilson syndrome due to monosomy 2q22
• Peripheral demyelinating neuropathy, central dysmyelinating leukodystrophy, Waardenburg syndrome, Hirschsprung disease
• Secondary megacolon - congenital
• Short segment Hirschsprung's disease
• Total colonic aganglionosis
• Total intestinal aganglionosis
• Waardenburg Shah syndrome
• Waardenburg syndrome
• Waardenburg syndrome

Diagnostic Related Group(s)

The code Q43.1 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)

• Other Digestive System Diagnoses With Mcc (393)
• Other Digestive System Diagnoses With Cc (394)
• Other Digestive System Diagnoses Without Cc/mcc (395)

References to Index of Diseases and Injuries

The code Q43.1 has the following ICD-10-CM references to the Index of Diseases and Injuries

• Inclusion Terms:
  • Aganglionosis
  • Congenital (aganglionic) megacolon

Crosswalk Information

Similar Codes

This page was last updated on: 10/1/2023

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