Diagnosis Code: Q56.1

Short Description: Male pseudohermaphroditism, not elsewhere classified

Long Description: Male pseudohermaphroditism, not elsewhere classified

The code Q56.1 is VALID for claim submission

Code Classification:

• Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • Congenital malformations of genital organs (Q50-Q56)
    • Indeterminate sex and pseudohermaphroditism (Q56)
      • Q56.1 Male pseudohermaphroditism, not elsewhere classified

This code is valid for diagnoses for males only

Code Version: 2022 ICD-10-CM

Synonyms

• 3-Oxo-5 alpha-steroid delta 4-dehydrogenase deficiency
• 46 XY disorder of sex development due to maternal ingestion of estrogen
• 46,XY disorder of sex development
• 46,XY disorder of sex development
• 46,XY disorder of sex development
• 46,XY disorder of sex development due to maternal ingestion of progestogen
• 46,XY disorder of sex development, adrenal insufficiency due to CYP11A1 deficiency
• 46,XY gonadal dysgenesis, motor and sensory neuropathy syndrome
• 46,XY ovotesticular disorder of sex development
• 46,XY partial gonadal dysgenesis
• Male pseudohermaphroditism
• Mixed sensory-motor polyneuropathy
• Motor polyneuropathy
• Ovotesticular disorder of sex development
• Rudimentary uterus in male
• Sensory polyneuropathy

Diagnostic Related Group(s)

The code Q56.1 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)

• Other Male Reproductive System Diagnoses With Cc/mcc (729)
• Other Male Reproductive System Diagnoses Without Cc/mcc (730)

References to Index of Diseases and Injuries

The code Q56.1 has the following ICD-10-CM references to the Index of Diseases and Injuries

• Inclusion Terms:
  • 46, XY with streak gonads
  • Male pseudohermaphroditism NOS

Crosswalk Information

Similar Codes

This page was last updated on: 10/1/2023

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