Diagnosis Code

C96.0 MULTIFOCAL AND MULTISYSTEMIC LANGERHANS-CELL HISTIOCYTOSIS


Code Information

Diagnosis Code: C96.0

Short Description: Multifocal and multisystemic Langerhans-cell histiocytosis

Long Description: Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis

The code C96.0 is VALID for claim submission

Code Classification:

  • Neoplasms (C00–D49)
    • Malignant neoplasms of lymphoid, hematopoietic and related tissue (C81-C96)
      • Oth & unsp malig neoplm of lymphoid, hematpoetc and rel tiss (C96)
        • C96.0 Multifocal and multisystemic Langerhans-cell histiocytosis

Code Version: 2022 ICD-10-CM


Synonyms

  • Langerhans cell histiocytosis, disseminated
  • Letterer-Siwe disease of intra-abdominal lymph nodes
  • Letterer-Siwe disease of intrapelvic lymph nodes
  • Letterer-Siwe disease of intrathoracic lymph nodes
  • Letterer-Siwe disease of lymph nodes of head
  • Letterer-Siwe disease of lymph nodes of head and neck
  • Letterer-Siwe disease of lymph nodes of lower limb
  • Letterer-Siwe disease of lymph nodes of multiple sites
  • Letterer-Siwe disease of lymph nodes of neck
  • Letterer-Siwe disease of lymph nodes of upper limb
  • Letterer-Siwe disease of spleen

References to Index of Diseases and Injuries

The code C96.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Histiocytosis X, multisystemic
    • Letterer-Siwe disease
  • Type 1 Excludes Notes:
    • adult pulmonary Langerhans cell histiocytosis (@J84.82*)
    • multifocal and unisystemic Langerhans-cell histiocytosis (@C96.5*)
    • unifocal Langerhans-cell histiocytosis (@C96.6*)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
C96.0 Right Arrow 202.50 Ltr-siwe unsp xtrndl org

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
C96 Other and unspecified malignant neoplasms of lymphoid, hematopoietic and related tissue
C96.2 Malignant mast cell neoplasm
C96.20 Malignant mast cell neoplasm, unspecified
C96.21 Aggressive systemic mastocytosis
C96.22 Mast cell sarcoma
C96.29 Other malignant mast cell neoplasm
C96.4 Sarcoma of dendritic cells (accessory cells)
C96.5 Multifocal and unisystemic Langerhans-cell histiocytosis
C96.6 Unifocal Langerhans-cell histiocytosis
C96.9 Malignant neoplasm of lymphoid, hematopoietic and related tissue, unspecified
C96.A Histiocytic sarcoma
C96.Z Other specified malignant neoplasms of lymphoid, hematopoietic and related tissue


This page was last updated on: 10/1/2023