Diagnosis Code

Q26.0 CONGENITAL STENOSIS OF VENA CAVA


Code Information

Diagnosis Code: Q26.0

Short Description: Congenital stenosis of vena cava

Long Description: Congenital stenosis of vena cava

The code Q26.0 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of the circulatory system (Q20-Q28)
      • Congenital malformations of great veins (Q26)
        • Q26.0 Congenital stenosis of vena cava

Code Version: 2022 ICD-10-CM


Synonyms

  • Abnormality of right superior vena cava
  • Congenital stenosis of inferior vena cava
  • Congenital stenosis of superior vena cava
  • Congenital stenosis of vena cava
  • Inferior vena cava stenosis
  • Superior vena cava stenosis

Diagnostic Related Group(s)

The code Q26.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Cardiac Congenital And Valvular Disorders With Mcc (306)
  • Cardiac Congenital And Valvular Disorders Without Mcc (307)

References to Index of Diseases and Injuries

The code Q26.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Congenital stenosis of vena cava (inferior)(superior)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q26.0 Right Arrow 747.49 Great vein anomaly NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q26 Congenital malformations of great veins
Q26.1 Persistent left superior vena cava
Q26.2 Total anomalous pulmonary venous connection
Q26.3 Partial anomalous pulmonary venous connection
Q26.4 Anomalous pulmonary venous connection, unspecified
Q26.5 Anomalous portal venous connection
Q26.6 Portal vein-hepatic artery fistula
Q26.8 Other congenital malformations of great veins
Q26.9 Congenital malformation of great vein, unspecified


This page was last updated on: 10/1/2023