Diagnosis Code

Q26.8 OTHER CONGENITAL MALFORMATIONS OF GREAT VEINS


Code Information

Diagnosis Code: Q26.8

Short Description: Other congenital malformations of great veins

Long Description: Other congenital malformations of great veins

The code Q26.8 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of the circulatory system (Q20-Q28)
      • Congenital malformations of great veins (Q26)
        • Q26.8 Other congenital malformations of great veins

Code Version: 2022 ICD-10-CM


Synonyms

  • Abnormal inferior vena caval connection
  • Abnormality of right inferior caval vein
  • Abnormality of right inferior caval vein
  • Abnormality of right inferior caval vein
  • Abnormality of right superior vena cava
  • Abnormality of right superior vena cava
  • Abnormality of right superior vena cava
  • Abnormality of right superior vena cava
  • Abnormality of right superior vena cava
  • Abnormality of right superior vena cava
  • Absence of inferior vena cava
  • Absence of superior vena cava
  • Absence of superior vena cava
  • Absence of superior vena cava
  • Absent bridging vein
  • Absent right superior vena cava
  • Anomalous insertion of right superior vena cava to left atrium
  • Atresia of left superior caval vein
  • Atresia of systemic vein
  • Atresia of systemic vein
  • Atresia of systemic vein
  • Atresia of systemic vein
  • Atresia of systemic vein
  • Atresia of systemic vein
  • Atresia of systemic vein
  • Atresia of systemic vein
  • Atretic right superior vena cava
  • Azygos continuation of inferior caval vein to right superior caval vein
  • Bilateral superior vena cava
  • Congenital abnormality of great veins and coronary sinus
  • Congenital abnormality of great veins and coronary sinus
  • Congenital abnormality of great veins and coronary sinus
  • Congenital abnormality of hepatic vein
  • Congenital absence of inferior vena cava
  • Congenital absence of superior vena cava
  • Congenital absence of vena cava
  • Congenital atresia of inferior vena cava
  • Congenital atresia of inferior vena cava without azygos continuation
  • Congenital atresia of superior vena cava
  • Congenital azygos continuation of inferior vena cava
  • Congenital dilatation of inferior vena cava
  • Congenital dilatation of superior vena cava
  • Congenital hypoplasia of cardiac vein
  • Congenital hypoplasia of pulmonary artery
  • Congenital hypoplasia of pulmonary artery
  • Congenital malposition of inferior vena cava
  • Congenital malposition of superior vena cava
  • Congenital pulmonary venous atrium
  • Congenital stenosis of pulmonary veins
  • Congenital systemic venous atrium
  • Hypoplasia of cardiac vein
  • Inferior cava to left of spine with right descending aorta
  • Inferior caval vein anterior and same side as descending aorta
  • Inferior caval vein connecting to right atrium and left atrium
  • Inferior vena cava connecting to coronary sinus
  • Inferior vena cava connecting to morphological left atrium
  • Inferior vena cava interruption with bilateral azygos continuation
  • Inferior vena cava interruption with left sided hemiazygos continuation
  • Inferior vena cava interruption with right sided azygos continuation
  • Inferior vena cava to left of spine
  • Interrupted left inferior caval vein
  • Interrupted right inferior caval vein
  • Left inferior caval vein connecting to left atrium and right atrium
  • Left sided azygos continuation of inferior caval vein to left superior caval vein
  • Obstructed anomalous pulmonary venous pathway
  • Obstructive Eustachian valve
  • Persistent common pulmonary vein
  • Persistent Eustachian valve
  • Persistent left posterior cardinal vein
  • Prolapse of Eustachian valve
  • Prominent valve of inferior vena cava
  • Prominent valve of inferior vena cava
  • Pulmonary hypertension due to developmental abnormality
  • Pulmonary vein stenosis
  • Pulmonary venous hypertension due to congenital stenosis of pulmonary vein
  • Pulmonary venous hypoplasia
  • Right inferior caval vein connecting to left atrium and right atrium
  • Right inferior caval vein connecting to left sided atrium
  • Right superior caval vein connecting to coronary sinus
  • Right superior caval vein connecting to coronary sinus
  • Right superior caval vein connecting to coronary sinus
  • Right superior caval vein connecting to coronary sinus and then to left sided atrium
  • Right superior caval vein connecting to left atrium and right atrium
  • Right superior caval vein persisting to coronary sinus and then to right sided atrium
  • Right ventricular outflow tract obstruction due to prolapse of Eustachian valve
  • Scimitar syndrome
  • Scimitar syndrome
  • Scimitar syndrome with additional anomalous pulmonary venous connection
  • Separate hepatic venous and inferior caval venous connections to heart
  • Sinus venosus atrial septal defect
  • Sinus venosus atrial septal defect
  • Sinus venosus defect with overriding inferior vena cava
  • Sinus venosus defect with overriding superior vena cava
  • Transposition of inferior vena cava
  • Venous remnant
  • Venous valvular anomaly
  • Venous valvular anomaly
  • Venous valvular anomaly

Diagnostic Related Group(s)

The code Q26.8 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Cardiac Congenital And Valvular Disorders With Mcc (306)
  • Cardiac Congenital And Valvular Disorders Without Mcc (307)

References to Index of Diseases and Injuries

The code Q26.8 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Absence of vena cava (inferior) (superior)
    • Azygos continuation of inferior vena cava
    • Persistent left posterior cardinal vein
    • Scimitar syndrome

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q26.8 Right Arrow 747.49 Great vein anomaly NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q26 Congenital malformations of great veins
Q26.0 Congenital stenosis of vena cava
Q26.1 Persistent left superior vena cava
Q26.2 Total anomalous pulmonary venous connection
Q26.3 Partial anomalous pulmonary venous connection
Q26.4 Anomalous pulmonary venous connection, unspecified
Q26.5 Anomalous portal venous connection
Q26.6 Portal vein-hepatic artery fistula
Q26.9 Congenital malformation of great vein, unspecified


This page was last updated on: 10/1/2023