Diagnosis Code

Q82.8 OTHER SPECIFIED CONGENITAL MALFORMATIONS OF SKIN


Code Information

Diagnosis Code: Q82.8

Short Description: Other specified congenital malformations of skin

Long Description: Other specified congenital malformations of skin

The code Q82.8 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Other congenital malformations of skin (Q82)
        • Q82.8 Other specified congenital malformations of skin

Code Version: 2022 ICD-10-CM


Synonyms

  • Abnormal blue sclerae
  • Abnormal dermatoglyphic pattern
  • Abnormal palmar creases
  • Abnormal plantar creases
  • Absence of fingerprints with congenital milia syndrome
  • Acanthosis nigricans
  • Acanthosis nigricans
  • Achondrogenesis
  • Achondroplasia
  • Acral Darier's disease
  • Acral peeling skin syndrome
  • Acrocyanosis
  • Acroerythrokeratoderma
  • Acrokerato-elastoidosis
  • Acrokeratosis verruciformis of Darier disease
  • Acrokeratosis verruciformis of Hopf
  • Acromegaloid phenotype with cutis verticis gyrata and corneal leukoma
  • Acroosteolysis
  • Alopecia, nail dystrophy, ophthalmic complications, thyroid dysfunction, hypohidrosis, ephelides, enteropathy and respiratory tract infections
  • Alveolar bone loss
  • Ambiguous genitalia
  • Angiomatosis
  • Aplasia cutis congenita secondary to malformation syndrome
  • Arrhythmogenic right ventricular dysplasia
  • Autosomal dominant complex hereditary spastic paraplegia
  • Autosomal dominant diffuse palmoplantar keratoderma Norrbotten type
  • Autosomal dominant dyskeratosis congenita
  • Autosomal dominant focal non-epidermolytic palmoplantar keratoderma with plantar blistering
  • Autosomal dominant ichthyosis
  • Autosomal dominant palmoplantar keratoderma and congenital alopecia
  • Autosomal dominant pseudoxanthoma elasticum
  • Autosomal recessive cutis laxa type 2A
  • Autosomal recessive cutis laxa type 2B
  • Autosomal recessive dyskeratosis congenita
  • Autosomal recessive familial wooly hair
  • Autosomal recessive familial wooly hair
  • Autosomal recessive familial wooly hair
  • Autosomal recessive hypohidrotic ectodermal dysplasia syndrome
  • Autosomal recessive palmoplantar keratoderma and congenital alopecia syndrome
  • Autosomal recessive pseudoxanthoma elasticum
  • Benign acanthosis nigricans
  • Bloom syndrome
  • Blue nevus of skin
  • Brugsch's syndrome
  • CAMOS syndrome
  • CEDNIK syndrome
  • Central cleft lip
  • Chronic hemolytic anemia
  • Circumscribed palmoplantar keratoderma
  • Circumscribed palmoplantar keratoderma
  • Clubbing of nail
  • Cole disease
  • Congenital absence of skin on scalp
  • Congenital absence of skin on scalp with epidermal nevi
  • Congenital accessory skin tag
  • Congenital anomaly of oral mucosa
  • Congenital anomaly of oral mucosa
  • Congenital anomaly of sclera
  • Congenital atrophy of optic nerve
  • Congenital clinodactyly
  • Congenital clinodactyly of finger
  • Congenital clinodactyly of little finger
  • Congenital clubnail
  • Congenital corneal leukoma
  • Congenital cutaneous angiomatosis
  • Congenital deficiency of pigment of skin
  • Congenital dermal sinus
  • Congenital ectodermal defect
  • Congenital erosive and vesicular dermatosis
  • Congenital extramedullary dermal hematopoiesis
  • Congenital hypotrichia
  • Congenital keratoderma
  • Congenital keratoderma
  • Congenital keratoderma
  • Congenital lethal erythroderma
  • Congenital leukonychia
  • Congenital livedo reticularis
  • Congenital melanosis
  • Congenital oculocutaneous hypopigmentation
  • Congenital palmoplantar and perioral keratoderma of Olmsted
  • Congenital pigmentary skin anomalies
  • Congenital retrognathism
  • Congenital scar
  • Congenital skin contracture
  • Congenital wooly hair
  • Congenital wooly hair
  • Congenital wooly hair
  • Congenital wooly hair
  • Connective tissue nevus of skin
  • Corneal intraepithelial dyskeratosis, palmoplantar hyperkeratosis, laryngeal dyskeratosis syndrome
  • Corneal leukoma
  • Craniofaciofrontodigital syndrome
  • Craniosynostosis, anal anomaly, porokeratosis syndrome
  • Curly hair, acral keratoderma, caries syndrome
  • Cutaneous lesion resulting from spina bifida
  • Cutis gyrata syndrome of Beare and Stevenson
  • Cutis laxa
  • Cutis laxa secondary to inherited disorder of connective tissue
  • Cutis laxa with osteodystrophy
  • Cutis laxa with severe pulmonary, gastrointestinal and urinary anomalies
  • Cutis laxa, autosomal dominant
  • Cutis laxa, autosomal recessive
  • Cutis laxa, autosomal recessive
  • Cutis laxa, autosomal recessive
  • Cutis laxa, recessive, type I
  • Cutis laxa, recessive, type II
  • Cutis verticis gyrata
  • Cutis verticis gyrata
  • Cyanosis of skin and/or skin-associated mucous membrane
  • Darier disease
  • Deaf blind hypopigmentation syndrome Yemenite type
  • Dermatitis of the newborn
  • Dermatoglyphs - skin lines
  • Dermatoleukodystrophy
  • Dermatopathia pigmentosa reticularis
  • Dermodental dysplasia
  • Diffuse dermatitis
  • Diffuse palmoplantar keratoderma and acrocyanosis syndrome
  • Diffuse palmoplantar keratoderma of Thost-Unna
  • Diffuse palmoplantar keratoderma with painful fissures
  • Disseminated superficial porokeratosis
  • Dwarfism, alopecia, pseudoanodontia, cutis laxa
  • Dyschromatosis universalis
  • Dyskeratosis congenita
  • Dysplasia of larynx
  • Eosinophilic pustular folliculitis
  • Epidermolytic palmoplantar keratoderma of Vorner
  • Erythrokeratoderma
  • Erythrokeratoderma progressiva of Gottron
  • Erythrokeratodermia cardiomyopathy syndrome
  • Erythrokeratodermia variabilis
  • Exostosis, anetoderma, brachydactyly type E syndrome
  • Extensive congenital erosions, vesicles and reticulate scarring
  • Extramedullary hematopoiesis
  • Facial dysmorphism, cleft palate, loose skin syndrome
  • Familial benign pemphigus
  • Familial generalized lentiginosis
  • Familial progressive hyper and hypopigmentation
  • Fat hypertrophy
  • Finding of palmar crease
  • Flexural Darier's disease
  • Flynn-Aird syndrome
  • Focal acral hyperkeratosis
  • Focal acral hyperkeratosis
  • Focal acral hyperkeratosis
  • Focal acral hyperkeratosis
  • Focal dermal hypoplasia
  • Focal palmoplantar and gingival keratoderma
  • Focal palmoplantar keratoderma with joint keratoses
  • Frontonasal dysplasia sequence
  • Genetic syndrome with hypermelanosis
  • Genodermatosis
  • Giant porokeratosis
  • Hair discoloration
  • Hairy malformation of palms and soles
  • Hemolytic anemia with emphysema AND cutis laxa
  • Hereditary acantholytic dermatosis
  • Hereditary acantholytic dermatosis
  • Hereditary acantholytic dermatosis
  • Hereditary acantholytic dermatosis
  • Hereditary acantholytic dermatosis
  • Hereditary acantholytic dermatosis
  • Hereditary acantholytic dermatosis
  • Hereditary acantholytic dermatosis
  • Hereditary acantholytic dermatosis
  • Hereditary acroosteolysis
  • Hereditary benign acanthosis nigricans
  • Hereditary benign acanthosis nigricans with insulin resistance
  • Hereditary benign intraepithelial dyskeratosis
  • Hereditary clubbing
  • Hereditary congenital hypomelanotic and hypermelanotic cutaneous macules, growth retardation, intellectual disability syndrome
  • Hereditary diffuse palmoplantar keratoderma
  • Hereditary erythrokeratolysis
  • Hereditary follicular keratoses
  • Hereditary palmoplantar keratoderma
  • Hereditary palmoplantar keratoderma Gamborg Nielsen type
  • Hereditary sclerosing poikiloderma
  • Hereditary sclerosing poikiloderma of Weary
  • Hereditary sensorimotor neuropathy with hyperelastic skin
  • Hereditary skin peeling syndrome
  • Hidrotic ectodermal dysplasia Christianson Fourie type
  • Hidrotic ectodermal dysplasia Halal type
  • Hidrotic ectodermal dysplasia syndrome
  • Howel-Evans' syndrome
  • Hoyeraal-Hreidarsson syndrome
  • Hyperplasia of gingiva
  • Hypertrophic Darier's disease
  • Hypohidrosis
  • Hypohidrosis, enamel hypoplasia, palmoplantar keratoderma, intellectual disability syndrome
  • Hypoplasia of thumb
  • Hypotrichosis with keratosis pilaris and lentiginosis
  • Hypotrichosis, osteolysis, periodontitis, palmoplantar keratoderma syndrome
  • Inherited cutaneous hyperpigmentation
  • Inherited cutis laxa
  • Inherited disorder of keratinization
  • Inherited pseudoxanthoma elasticum
  • Insulin receptor defect
  • Isolated congenital adermatoglyphia
  • Isolated focal non-epidermolytic palmoplantar keratoderma
  • Juvenile elastoma
  • Keratoderma
  • Keratoderma hereditarium mutilans with ichthyosis syndrome
  • Keratolysis exfoliativa
  • Keratolytic winter erythema
  • Keratosis follicularis, dwarfism, cerebral atrophy syndrome
  • Keratosis linearis, ichthyosis congenita, sclerosing keratoderma syndrome
  • Keratosis pilaris
  • Keratosis pilaris
  • Keratosis pilaris atrophicans
  • Keratosis pilaris decalvans
  • Keratosis rubra pilaris
  • Kindler's syndrome
  • Kohlschutter's syndrome
  • KRT1-related diffuse nonepidermolytic keratoderma
  • Leukonychia totalis
  • Leukonychia totalis, acanthosis-nigricans-like lesions, abnormal hair syndrome
  • Lichen spinulosus
  • Linear porokeratosis
  • Linear/nevoid/zosteriform Darier's disease
  • Lipoma of brain
  • Livedo reticularis
  • Localized congenital cutis laxa
  • Macroencephaly
  • MACS syndrome
  • Malignant melanoma arising in congenital nevus
  • Mass of palm
  • MEDNIK syndrome
  • Megalencephaly capillary malformation
  • Melanin pigmentation of oral mucosa
  • Melanosis of mucosa of body orifice
  • Michelin-tire baby
  • Microphthalmia with linear skin defect syndrome
  • Microphthalmos due to Delleman syndrome
  • Milia
  • Mongolian spot
  • Multiple benign annular creases of extremities
  • Multiple lentigines syndrome
  • Multiple malformation syndrome with senile-like appearance
  • Multiple malformation syndrome with senile-like appearance
  • Multiple malformation syndrome with senile-like appearance
  • Multiple malformation syndrome, small stature, without skeletal dysplasia
  • Mutilating keratoderma
  • Mutilating keratoderma
  • Naegeli-Franceschetti-Jadassohn syndrome
  • Nail and tooth abnormalities, marginal palmoplantar keratoderma, oral hyperpigmentation syndrome
  • Nail dystrophy due to benign familial pemphigus
  • Nail dystrophy due to Darier's disease
  • Naxos disease
  • Neonatal cutis laxa with marfanoid phenotype
  • Neonatal eosinophilic pustular folliculitis
  • Neuroectodermal melanolysosomal disease
  • Nevus elasticus
  • Oculocerebrocutaneous syndrome
  • Osteopathia striata
  • Osteopathia striata, pigmentary dermopathy, white forelock syndrome
  • Osteoporosis and oculocutaneous hypopigmentation syndrome
  • Otopalatodigital syndrome spectrum disorder
  • Pai syndrome
  • Palmar pit
  • Palmar pitting due to Darier disease
  • Palmoplantar hyperkeratosis sclerodactyly syndrome
  • Palmoplantar hyperkeratosis-hyperpigmentation syndrome of Cantu
  • Palmoplantar keratoderma
  • Palmoplantar keratoderma Nagashima type
  • Palmoplantar keratoderma transgrediens
  • Palmoplantar keratoderma with clinodactyly syndrome
  • Palmoplantar keratoderma with deafness syndrome
  • Palmoplantar keratoderma, 46,XX sex reversal, predisposition to squamous cell carcinoma syndrome
  • Palmoplantar keratoderma, hereditary motor and sensory neuropathy syndrome
  • Palmoplantar keratoderma, spastic paralysis syndrome
  • Papillon-Lefèvre syndrome
  • Papular epidermal nevi with skyline basal cell layers syndrome
  • Papuloverrucous palmoplantar keratoderma of Jakac-Wolf
  • Peripheral cyanosis
  • Pigmentation defects, palmoplantar keratoderma, skin carcinoma syndrome
  • Poikiloderma, alopecia, retrognathism, cleft palate syndrome
  • Porokeratosis
  • Porokeratosis of Mibelli
  • Porokeratosis plantaris palmaris et disseminata
  • Preauricular dimple
  • Primary essential cutis verticis gyrata
  • Primary non-essential cutis verticis gyrata
  • Progressive palmoplantar keratoderma of Greither
  • Pseudoxanthoma elasticum
  • Punctate palmoplantar keratoderma
  • Punctate palmoplantar keratoderma
  • Punctate palmoplantar keratoderma
  • Punctate palmoplantar keratoderma type 1
  • Reticulate pigmented anomaly of flexures
  • Rothmund Thomson syndrome type 1
  • Rothmund Thomson syndrome type 2
  • Rothmund-Thomson syndrome
  • SCARF syndrome
  • Severe achondroplasia, developmental delay, acanthosis nigricans syndrome
  • Severe dermatitis, multiple allergies, metabolic wasting syndrome
  • Severe growth deficiency, strabismus, extensive dermal melanocytosis, intellectual disability syndrome
  • Single transverse palmar crease
  • Skin fragility, wooly hair, palmoplantar keratoderma syndrome
  • Skin peeling disorder
  • Skin punctum
  • Spastic paraplegia, intellectual disability, palmoplantar hyperkeratosis syndrome
  • Spastic paraplegia, neuropathy, poikiloderma syndrome
  • Striate palmoplantar keratoderma
  • Symmetrical dyschromatosis of extremities
  • Systematized linear porokeratosis
  • Talipes cavus
  • Terminal osseous dysplasia and pigmentary defect syndrome
  • Thumb deformity, alopecia, pigmentation anomaly syndrome
  • Torticollis, keloids, cryptorchidism, renal dysplasia syndrome
  • Trichodental syndrome
  • Trichothiodystrophy
  • Variation in hair color
  • Vascular neurocutaneous syndrome
  • White forelock
  • Wooly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome
  • Wooly hair with palmoplantar keratoderma syndrome
  • Wrinkly skin syndrome
  • X-linked dyskeratosis congenita
  • Zosteriform lentiginosis

Diagnostic Related Group(s)

The code Q82.8 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Minor Skin Disorders With Mcc (606)
  • Minor Skin Disorders Without Mcc (607)

References to Index of Diseases and Injuries

The code Q82.8 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Abnormal palmar creases
    • Accessory skin tags
    • Benign familial pemphigus [Hailey-Hailey]
    • Congenital poikiloderma
    • Cutis laxa (hyperelastica)
    • Dermatoglyphic anomalies
    • Inherited keratosis palmaris et plantaris
    • Keratosis follicularis [Darier-White]
  • Type 1 Excludes Notes:
    • Ehlers-Danlos syndromes (@Q79.6*-)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q82.8 Right Arrow 757.2 Dermatoglyphic anomalies
757.39 Skin anomaly NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q82 Other congenital malformations of skin
Q82.0 Hereditary lymphedema
Q82.1 Xeroderma pigmentosum
Q82.2 Congenital cutaneous mastocytosis
Q82.3 Incontinentia pigmenti
Q82.4 Ectodermal dysplasia (anhidrotic)
Q82.5 Congenital non-neoplastic nevus
Q82.6 Congenital sacral dimple
Q82.9 Congenital malformation of skin, unspecified


This page was last updated on: 10/1/2023