046.19 CREUTZFLDT-JAKOB NEC/NOS

Code Information

Diagnosis Code: 046.19

Short Description: Creutzfldt-Jakob NEC/NOS

Long Description: Other and unspecified Creutzfeldt-Jakob disease

Code Classification:

  • Infectious and parasitic diseases (001–139)
    • Poliomyelitis and other non-arthropod-borne viral diseases of central nervous system (045-049)
      • 046 Slow virus infection of central nervous system
        • 046.19 Creutzfldt-Jakob NEC/NOS

Code Version: 2015 ICD-9-CM

Synonyms

  • Cerebral degeneration due to Creutzfeldt-Jakob disease
  • Dementia due to Creutzfeldt Jakob disease
  • Jakob-Creutzfeldt disease
  • Spongiform encephalopathy

References to Index of Diseases and Injuries

The code 046.19 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • CJD (Creutzfeldt-Jakob disease) 046.19
    • variant (vCJD) 046.11
  • Creutzfeldt-Jakob disease (CJD) (syndrome) 046.19
    • with dementia
      • with behavioral disturbance 046.19 [294.11]
      • without behavioral disturbance 046.19 [294.10]
    • familial 046.19
    • iatrogenic 046.19
    • specified NEC 046.19
    • sporadic 046.19
    • variant (vCJD) 046.11
      • with dementia
        • with behavioral disturbance 046.11 [294.11]
        • without behavioral disturbance 046.11 [294.10]
  • Dementia 294.20
    • due to or associated with condition(s) classified elsewhere
      • Jakob-Creutzfeldt disease (CJD)
        • with behavioral disturbance 046.19 [294.11]
        • without behavioral disturbance 046.19 [294.10]
  • Disease, diseased - see also Syndrome
    • Creutzfeldt-Jakob (CJD) 046.19
      • with dementia
        • with behavioral disturbance 046.19 [294.11]
        • without behavioral disturbance 046.19 [294.10]
      • familial 046.19
      • iatrogenic 046.19
      • specified NEC 046.19
      • sporadic 046.19
      • variant (vCJD) 046.11
        • with dementia
          • with behavioral disturbance 046.11 [294.11]
          • without behavioral disturbance 046.11 [294.10]
    • Jakob-Creutzfeldt (CJD) 046.19
      • with dementia
        • with behavioral disturbance 046.19 [294.11]
        • without behavioral disturbance 046.19 [294.10]
      • familial 046.19
      • iatrogenic 046.19
      • specified NEC 046.19
      • sporadic 046.19
      • variant (vCJD) 046.11
        • with dementia
          • with behavioral disturbance 046.11 [294.11]
          • without behavioral disturbance 046.11 [294.10]
  • Encephalopathy (acute) 348.30
    • spongioform, subacute (viral) 046.19
    • subacute
      • spongioform 046.19
      • viral, spongioform 046.19
  • Jakob-Creutzfeldt disease (CJD) (syndrome) 046.19
    • with dementia
      • with behavioral disturbance 046.19 [294.11]
      • without behavioral disturbance 046.19 [294.10]
    • familial 046.19
    • iatrogenic 046.19
    • specified NEC 046.19
    • sporadic 046.19
    • variant (vCJD) 046.11
      • with dementia
        • with behavioral disturbance 046.11 [294.11]
        • without behavioral disturbance 046.11 [294.10]
  • Pseudosclerosis (brain)
    • Jakob's 046.19
    • spastic 046.19
      • with dementia
        • with behavioral disturbance 046.19 [294.11]
        • without behavioral disturbance 046.19 [294.10]
  • Psychosis 298.9
    • organic NEC 294.9
      • due to or associated with
        • disease
          • Jakob-Creutzfeldt 046.19
            • with behavioral disturbance 046.19 [294.11]
            • without behavioral disturbance 046.19 [294.10]
            • familial 046.19
            • iatrogenic 046.19
            • specified NEC 046.19
            • sporadic 046.19
            • variant 046.11
              • with dementia
                • with behavioral disturbance 046.11 [294.11]
                • without behavioral disturbance 046.11 [294.10]
        • Jakob-Creutzfeldt disease (syndrome) 046.19
          • with behavioral disturbance 046.19 [294.11]
          • without behavioral disturbance 046.19 [294.10]
          • variant 046.11
            • with dementia
              • with behavioral disturbance 046.11 [294.11]
              • without behavioral disturbance 046.11 [294.10]
  • Syndrome - see also Disease
    • Creutzfeldt-Jakob 046.19
      • with dementia
        • with behavioral disturbance 046.19 [294.11]
        • without behavioral disturbance 046.19 [294.10]
      • variant 046.11
        • with dementia
          • with behavioral disturbance 046.11 [294.11]
          • without behavioral disturbance 046.11 [294.10]
    • Jakob-Creutzfeldt 046.19
      • with dementia
        • with behavioral disturbance 046.19 [294.11]
        • without behavioral disturbance 046.19 [294.10]
      • variant 046.11
        • with dementia
          • with behavioral disturbance 046.11 [294.11]
          • without behavioral disturbance 046.11 [294.10]

Crosswalk Information

The code 046.19 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
046.19 Right Arrow A81.00 Creutzfeldt-Jakob disease, unspecified
A81.09 Other Creutzfeldt-Jakob disease
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
046.0 Kuru
046.11 Variant Creutzfeldt-Jakob disease
046.2 Subacute sclerosing panencephalitis
046.3 Progressive multifocal leukoencephalopathy
046.71 Gerstmann-Str�ussler-Scheinker syndrome
046.72 Fatal familial insomnia
046.79 Other and unspecified prion disease of central nervous system
046.8 Other specified slow virus infection of central nervous system
046.9 Unspecified slow virus infection of central nervous system

This page was last updated on: 10/1/2014