270.6 DIS UREA CYCLE METABOL


Code Information

Diagnosis Code: 270.6

Short Description: Dis urea cycle metabol

Long Description: Disorders of urea cycle metabolism

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 270 Disorders of amino-acid transport and metabolism
        • 270.6 Dis urea cycle metabol

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 270.6 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Acidemia 276.2
    • arginosuccinic 270.6
  • Aciduria 791.9
    • arginosuccinic 270.6
  • Arginosuccinicaciduria 270.6
  • Citrullinemia 270.6
  • Citrullinuria 270.6
  • Deficiency, deficient
    • argininosuccinate synthetase or lyase 270.6
    • carbamyl phosphate synthetase 270.6
    • ornithine transcarbamylase 270.6
  • Disorder - see also Disease
    • amino acid (metabolic) (see also Disturbance, metabolism, amino acid) 270.9
      • argininosuccinicaciduria 270.6
    • metabolism NEC 277.9
      • ammonia 270.6
      • arginine 270.6
      • argininosuccinic acid 270.6
      • citrulline 270.6
      • ornithine 270.6
      • urea cycle 270.6
  • Disturbance - see also Disease
    • metabolism (acquired) (congenital) (see also Disorder, metabolism) 277.9
      • ammonia 270.6
      • arginine 270.6
      • argininosuccinic acid 270.6
      • citrulline 270.6
      • ornithine 270.6
      • urea cycle 270.6
  • Hyperaminoaciduria 270.9
    • arginine 270.6
    • citrulline 270.6
    • ornithine 270.6
  • Hyperammonemia (congenital) 270.6
  • Hyperornithinemia 270.6

Crosswalk Information

The code 270.6 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
270.6 Right Arrow E72.20 Disorder of urea cycle metabolism, unspecified
E72.22 Arginosuccinic aciduria
E72.23 Citrullinemia
E72.29 Other disorders of urea cycle metabolism
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
270.0 Disturbances of amino-acid transport
270.1 Phenylketonuria [PKU]
270.2 Other disturbances of aromatic amino-acid metabolism
270.3 Disturbances of branched-chain amino-acid metabolism
270.4 Disturbances of sulphur-bearing amino-acid metabolism
270.5 Disturbances of histidine metabolism
270.7 Other disturbances of straight-chain amino-acid metabolism
270.8 Other specified disorders of amino-acid metabolism
270.9 Unspecified disorder of amino-acid metabolism


This page was last updated on: 10/1/2014