271.2 HERED FRUCTOSE INTOLERAN


Code Information

Diagnosis Code: 271.2

Short Description: Hered fructose intoleran

Long Description: Hereditary fructose intolerance

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 271 Disorders of carbohydrate transport and metabolism
        • 271.2 Hered fructose intoleran

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 271.2 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Deficiency, deficient
    • aldolase (hereditary) 271.2
    • fructokinase 271.2
    • fructose-1, 6-diphosphate 271.2
    • fructose-1-phosphate aldolase 271.2
    • phosphofructokinase 271.2
  • Disorder - see also Disease
    • metabolism NEC 277.9
      • fructosemia 271.2
      • fructosuria 271.2
  • Disturbance - see also Disease
    • fructose metabolism 271.2
  • Fructosemia 271.2
  • Fructosuria (benign) (essential) 271.2
  • Hyperfructosemia 271.2
  • Intolerance
    • fructose (hereditary) 271.2
  • Levulosuria 271.2

Crosswalk Information

The code 271.2 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
271.2 Right Arrow E74.11 Essential fructosuria
E74.12 Hereditary fructose intolerance
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
271.0 Glycogenosis
271.1 Galactosemia
271.3 Intestinal disaccharidase deficiencies and disaccharide malabsorption
271.4 Renal glycosuria
271.8 Other specified disorders of carbohydrate transport and metabolism
271.9 Unspecified disorder of carbohydrate transport and metabolism


This page was last updated on: 10/1/2014