271.8 DIS CARBOHYDR METAB NEC


Code Information

Diagnosis Code: 271.8

Short Description: Dis carbohydr metab NEC

Long Description: Other specified disorders of carbohydrate transport and metabolism

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 271 Disorders of carbohydrate transport and metabolism
        • 271.8 Dis carbohydr metab NEC

Code Version: 2015 ICD-9-CM


Synonyms

  • Acquired monosaccharide malabsorption
  • Adult fucosidosis
  • alpha, alpha-Trehalase deficiency
  • Antifreeze oxalosis
  • Beta-D-mannosidosis
  • Carbohydrate-deficient glycoprotein syndrome
  • Carbohydrate-deficient glycoprotein syndrome type II
  • Carbohydrate-deficient glycoprotein syndrome type III
  • Congenital disorder of glycosylation type Ia
  • Congenital monosaccharide malabsorption
  • Deficiency of alpha-mannosidase
  • Disorder of carbohydrate absorption
  • Disorder of glucose metabolism
  • Disorder of glycerate metabolism
  • Dysglycemia
  • Enteric hyperoxaluria
  • Essential pentosuria
  • Fucosidosis
  • Hyperglycemic disorder
  • Impaired glucose tolerance associated with genetic syndrome
  • Impaired intestinal epithelial cell transport of carbohydrates
  • Infantile fucosidosis
  • Insulin resistance - type A
  • Insulin resistance - type B
  • Juvenile fucosidosis
  • Lactate dehydrogenase deficiency
  • Mannosidosis
  • Mannosidosis, type I
  • Mannosidosis, type II
  • Nonglucosuric melituria
  • Oxalosis
  • Primary hyperoxaluria
  • Primary hyperoxaluria, type I
  • Primary hyperoxaluria, type II
  • Secondary oxalosis
  • Syndrome of carbohydrate intolerance
  • Xylosuria

References to Index of Diseases and Injuries

The code 271.8 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Absence (organ or part) (complete or partial)
    • alpha-fucosidase 271.8
    • fucosidase 271.8
  • Aciduria 791.9
    • glycolic 271.8
  • Bird's disease (oxaluria) 271.8
  • Carbohydrate-deficient glycoprotein syndrome (CDGS) 271.8
  • CDGS (carbohydrate-deficient glycoprotein syndrome) 271.8
  • Deficiency, deficient
    • alpha-fucosidase 271.8
    • alpha-mannosidase 271.8
    • fucosidase 271.8
    • mannosidase 271.8
    • phosphoenolpyruvate carboxykinase 271.8
    • phosphomannomutase 271.8
    • phosphomannose isomerase 271.8
    • phosphomannosyl mutase 271.8
    • pyruvate carboxylase 271.8
    • pyruvate dehydrogenase 271.8
  • Diathesis
    • oxalic 271.8
  • Disease, diseased - see also Syndrome
    • Bird's (oxaluria) 271.8
  • Disorder - see also Disease
    • congenital
      • glycosylation (CDG) 271.8
    • infant sialic acid storage 271.8
    • metabolism NEC 277.9
      • carbohydrate 271.9
        • specified type NEC 271.8
      • fucosidosis 271.8
      • mannosidosis 271.8
      • oxalosis 271.8
      • pentosuria 271.8
      • xylose 271.8
    • transport, carbohydrate 271.9
      • specified type NEC 271.8
  • Fucosidosis 271.8
  • Hyperoxaluria (primary) 271.8
  • L-xyloketosuria 271.8
  • Malabsorption 579.9
    • monosaccharide 271.8
  • Mannoheptulosuria 271.8
  • Mannosidosis 271.8
  • Oxalosis 271.8
  • Oxaluria 271.8
  • Pentosuria (benign) (essential) 271.8
  • Syndrome - see also Disease
    • carbohydrate-deficient glycoprotein (CDGS) 271.8
  • Xyloketosuria 271.8
  • Xylosuria 271.8
  • Xylulosuria 271.8

Crosswalk Information

The code 271.8 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
271.8 Right Arrow E72.52 Trimethylaminuria
E72.53 Hyperoxaluria
E74.4 Disorders of pyruvate metabolism and gluconeogenesis
E74.8 Other specified disorders of carbohydrate metabolism
E77.1 Defects in glycoprotein degradation
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
271.0 Glycogenosis
271.1 Galactosemia
271.2 Hereditary fructose intolerance
271.3 Intestinal disaccharidase deficiencies and disaccharide malabsorption
271.4 Renal glycosuria
271.9 Unspecified disorder of carbohydrate transport and metabolism


This page was last updated on: 10/1/2014