277.1 DIS PORPHYRIN METABOLISM


Code Information

Diagnosis Code: 277.1

Short Description: Dis porphyrin metabolism

Long Description: Disorders of porphyrin metabolism

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 277 Other and unspecified disorders of metabolism
        • 277.1 Dis porphyrin metabolism

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 277.1 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Coproporphyria, hereditary 277.1
  • Disease, diseased - see also Syndrome
    • G�nther's (congenital erythropoietic porphyria) 277.1
  • Disorder - see also Disease
    • metabolism NEC 277.9
      • porphyrin 277.1
    • porphyrin metabolism 277.1
  • G�nther's disease or syndrome (congenital erythropoietic porphyria) 277.1
  • Hematoporphyria (acquired) (congenital) 277.1
  • Hematoporphyrinuria (acquired) (congenital) 277.1
  • Photocoproporphyria 277.1
  • Polyneuropathy (peripheral) 356.9
    • due to
      • porphyria 277.1 [357.4]
    • in
      • porphyria 277.1 [357.4]
  • Porphyria (acute) (congenital) (constitutional) (erythropoietic) (familial) (hepatica) (idiopathic) (idiosyncratic) (intermittent) (latent) (mixed hepatic) (photosensitive) (South African genetic) (Swedish) 277.1
    • acquired 277.1
    • cutaneatarda
      • hereditaria 277.1
      • symptomatica 277.1
    • due to drugs
      • correct substance properly administered 277.1
      • overdose or wrong substance given or taken 977.9
        • specified drug - see Table of Drugs and Chemicals
    • secondary 277.1
    • toxic NEC 277.1
    • variegata 277.1
  • Porphyrinuria (acquired) (congenital) (secondary) 277.1
  • Porphyruria (acquired) (congenital) 277.1
  • Protocoproporphyria 277.1
  • Protoporphyria (erythrohepatic) (erythropoietic) 277.1
  • Pyrroloporphyria 277.1
  • Syndrome - see also Disease
    • G�nther's (congenital erythropoietic porphyria) 277.1

Crosswalk Information

The code 277.1 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
277.1 Right Arrow E80.0 Hereditary erythropoietic porphyria
E80.20 Unspecified porphyria
E80.29 Other porphyria
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
277.00 Cystic fibrosis without mention of meconium ileus
277.01 Cystic fibrosis with meconium ileus
277.02 Cystic fibrosis with pulmonary manifestations
277.03 Cystic fibrosis with gastrointestinal manifestations
277.09 Cystic fibrosis with other manifestations
277.2 Other disorders of purine and pyrimidine metabolism
277.30 Amyloidosis, unspecified
277.31 Familial Mediterranean fever
277.39 Other amyloidosis
277.4 Disorders of bilirubin excretion
277.5 Mucopolysaccharidosis
277.6 Other deficiencies of circulating enzymes
277.7 Dysmetabolic syndrome X
277.81 Primary carnitine deficiency
277.82 Carnitine deficiency due to inborn errors of metabolism
277.83 Iatrogenic carnitine deficiency
277.84 Other secondary carnitine deficiency
277.85 Disorders of fatty acid oxidation
277.86 Peroxisomal disorders
277.87 Disorders of mitochondrial metabolism
277.88 Tumor lysis syndrome
277.89 Other specified disorders of metabolism
277.9 Unspecified disorder of metabolism


This page was last updated on: 10/1/2014