277.5 MUCOPOLYSACCHARIDOSIS


Code Information

Diagnosis Code: 277.5

Short Description: Mucopolysaccharidosis

Long Description: Mucopolysaccharidosis

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 277 Other and unspecified disorders of metabolism
        • 277.5 Mucopolysaccharidosis

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 277.5 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Brailsford-Morquio disease or syndrome (mucopolysaccharidosis IV) 277.5
  • Cardiomyopathy (congestive) (constrictive) (familial) (infiltrative) (obstructive) (restrictive) (sporadic) 425.4
    • due to
      • mucopolysaccharidosis 277.5 [425.7]
  • Cardiopathy (see also Disease, heart) 429.9
    • mucopolysaccharidosis 277.5 [425.7]
  • Chondrodystrophia (fetalis) 756.4
    • tarda 277.5
  • Chondro-osteodysplasia (Morquio-Brailsford type) 277.5
  • Chondro-osteodystrophy 277.5
  • Curvature
    • spine (acquired) (angular) (idiopathic) (incorrect) (postural) 737.9
      • due to or associated with
        • mucopolysaccharidosis 277.5 [737.40]
  • Degeneration, degenerative
    • brain (cortical) (progressive) 331.9
      • in
        • Hunter's disease or syndrome 277.5 [330.3]
        • mucopolysaccharidosis 277.5 [330.3]
  • Deposit
    • cornea, corneal NEC 371.10
      • in
        • mucopolysaccharidosis 277.5 [371.15]
  • Disease, diseased - see also Syndrome
    • Brailsford-Morquio (mucopolysaccharidosis IV) 277.5
    • heart (organic) 429.9
      • due to
        • mucopolysaccharidosis 277.5 [425.7]
    • Hurler's (mucopolysaccharidosis I) 277.5
    • Morquio (-Brailsford) (-Ullrich) (mucopolysaccharidosis IV) 277.5
    • storage
      • mucopolysaccharide 277.5
  • Disorder - see also Disease
    • metabolism NEC 277.9
      • mucopolysaccharide 277.5
    • mucopolysaccharide 277.5
  • Dwarf, dwarfism 259.4
    • polydystrophic 277.5
  • Dysostosis
    • multiplex 277.5
  • Dystrophy, dystrophia 783.9
    • familial
      • osseous 277.5
  • Eccentro-osteochondrodysplasia 277.5
  • Gargoylism 277.5
  • Heparitinuria 277.5
  • Hunter (-Hurler) syndrome (mucopolysaccharidosis II) 277.5
  • Hurler (-Hunter) disease or syndrome (mucopolysaccharidosis II) 277.5
  • Kyphosis, kyphotic (acquired) (postural) 737.10
    • due to or associated with
      • mucopolysaccharidosis 277.5 [737.41]
    • Morquio-Brailsford type (spinal) 277.5 [737.41]
  • Lipochondrodystrophy 277.5
  • Lordosis (acquired) (postural) 737.20
    • due to or associated with
      • mucopolysaccharidosis 277.5 [737.42]
  • Maroteaux-Lamy syndrome (mucopolysaccharidosis VI) 277.5
  • Morquio (-Brailsford) (-Ullrich) disease or syndrome (mucopolysaccharidosis IV) 277.5
    • kyphosis 277.5
  • Mucopolysaccharidosis (types 1-6) 277.5
    • cardiopathy 277.5 [425.7]
  • Myocardiopathy (congestive) (constrictive) (familial) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic) 425.4
    • due to
      • mucopolysaccharidosis 277.5 [425.7]
  • Osteochondrodystrophy 277.5
    • deformans 277.5
    • familial 277.5
    • fetalis 756.4
  • Polydystrophic oligophrenia 277.5
  • Sanfilippo's syndrome (mucopolysaccharidosis III) 277.5
  • Scheie's syndrome (mucopolysaccharidosis IS) 277.5
  • Scoliosis (acquired) (postural) 737.30
    • due to or associated with
      • mucopolysaccharidosis 277.5 [737.43]
  • Syndrome - see also Disease
    • Brailsford-Morquio (dystrophy) (mucopolysaccharidosis IV) 277.5
    • Hunter (-Hurler) (mucopolysaccharidosis II) 277.5
    • Hurler (-Hunter) (mucopolysaccharidosis II) 277.5
    • Maroteaux-Lamy (mucopolysaccharidosis VI) 277.5
    • Morquio (-Brailsford) (-Ullrich) (mucopolysaccharidosis IV) 277.5
    • Sanfilippo's (mucopolysaccharidosis III) 277.5
    • Scheie's (mucopolysaccharidosis IS) 277.5

Crosswalk Information

The code 277.5 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
277.5 Right Arrow E76.01 Hurler's syndrome
E76.03 Scheie's syndrome
E76.1 Mucopolysaccharidosis, type II
E76.219 Morquio mucopolysaccharidoses, unspecified
E76.22 Sanfilippo mucopolysaccharidoses
E76.29 Other mucopolysaccharidoses
E76.3 Mucopolysaccharidosis, unspecified
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
277.00 Cystic fibrosis without mention of meconium ileus
277.01 Cystic fibrosis with meconium ileus
277.02 Cystic fibrosis with pulmonary manifestations
277.03 Cystic fibrosis with gastrointestinal manifestations
277.09 Cystic fibrosis with other manifestations
277.1 Disorders of porphyrin metabolism
277.2 Other disorders of purine and pyrimidine metabolism
277.30 Amyloidosis, unspecified
277.31 Familial Mediterranean fever
277.39 Other amyloidosis
277.4 Disorders of bilirubin excretion
277.6 Other deficiencies of circulating enzymes
277.7 Dysmetabolic syndrome X
277.81 Primary carnitine deficiency
277.82 Carnitine deficiency due to inborn errors of metabolism
277.83 Iatrogenic carnitine deficiency
277.84 Other secondary carnitine deficiency
277.85 Disorders of fatty acid oxidation
277.86 Peroxisomal disorders
277.87 Disorders of mitochondrial metabolism
277.88 Tumor lysis syndrome
277.89 Other specified disorders of metabolism
277.9 Unspecified disorder of metabolism


This page was last updated on: 10/1/2014