277.6 DEFIC CIRCUL ENZYME NEC


Code Information

Diagnosis Code: 277.6

Short Description: Defic circul enzyme NEC

Long Description: Other deficiencies of circulating enzymes

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 277 Other and unspecified disorders of metabolism
        • 277.6 Defic circul enzyme NEC

Code Version: 2015 ICD-9-CM


Synonyms

  • 6-Pyruvoyl-tetrahydrobiopterin synthase deficiency
  • Acetyl-CoA: carboxylase deficiency
  • Acid phosphatase deficiency
  • Alpha-2-antitrypsin deficiency
  • Bifunctional peroxisomal enzyme deficiency
  • Biotinidase deficiency
  • Clinical manifestation of carnosinase deficiency
  • Clinical manifestation of enzyme deficiency
  • Combined deficiency of sialidase AND beta galactosidase
  • Complex V deficiency
  • Cytochrome p450 CYP1A2 enzyme deficiency
  • Cytochrome p450 CYP2C19 enzyme deficiency
  • Cytochrome p450 CYP2C9 enzyme deficiency
  • Cytochrome p450 CYP2D6 enzyme deficiency
  • Cytochrome p450 CYP2E1 enzyme deficiency
  • Cytochrome p450 CYP3A enzyme deficiency
  • Cytochrome p450 enzyme deficiency
  • Deficiency of
  • Deficiency of
  • Deficiency of 1,3-beta-glucan synthase
  • Deficiency of 1,4-alpha-glucan 6alpha-glucosyltransferase
  • Deficiency of 1,4-alpha-glucan branching enzyme
  • Deficiency of 2,4-dienoyl-coenzyme A reductase
  • Deficiency of 2,5-diaminovalerate aminotransferase
  • Deficiency of 2-hydroxyglutarate dehydrogenase
  • Deficiency of 2-methylbutyryl-coenzyme A dehydrogenase
  • Deficiency of 3alpha-hydroxycholanate dehydrogenase
  • Deficiency of 3alpha-hydroxysteroid dehydrogenase
  • Deficiency of 3-hydroxyacyl-CoA dehydrogenase
  • Deficiency of 3-hydroxybutyrate dehydrogenase
  • Deficiency of 3-hydroxybutyryl-coenzyme A epimerase
  • Deficiency of 3-hydroxyisobutyrate dehydrogenase
  • Deficiency of 3-hydroxyisobutyryl coenzyme A hydrolase
  • Deficiency of 3-mercaptopyruvate sulfurtransferase
  • Deficiency of 3'-nucleotidase
  • Deficiency of 3-oxoacid coenzyme A-transferase
  • Deficiency of 3-oxoadipate coenzyme A-transferase
  • Deficiency of 4-hydroxy-2-oxoglutarate aldolase
  • Deficiency of 5'-nucleotidase
  • Deficiency of 6-phosphofructokinase
  • Deficiency of A-ase
  • Deficiency of acetate kinase
  • Deficiency of acetate-coenzyme A ligase
  • Deficiency of acetoacetyl-coenzyme A reductase
  • Deficiency of acetylcholinesterase
  • Deficiency of acetyl-CoA hydrolase
  • Deficiency of acetyl-coenzyme A acetyltransferase
  • Deficiency of acetyl-coenzyme A acylase
  • Deficiency of acetyl-coenzyme A acyltransferase
  • Deficiency of acetyl-coenzyme A deacylase
  • Deficiency of acetylesterase
  • Deficiency of acetylserotonin methyltransferase
  • Deficiency of acid-aminoacid ligase
  • Deficiency of acid-ammonia ligase
  • Deficiency of aconitate hydratase
  • Deficiency of acylphosphatase
  • Deficiency of adenine deaminase
  • Deficiency of adenine phosphoribosyltransferase
  • Deficiency of adenosine diphosphate deaminase
  • Deficiency of adenosine kinase
  • Deficiency of adenosine monophosphate deaminase
  • Deficiency of adenosine monophosphate nucleosidase
  • Deficiency of adenosine triphosphate pyrophosphatase
  • Deficiency of adenosinetriphosphatase
  • Deficiency of adenosylhomocysteinase
  • Deficiency of adenylate kinase
  • Deficiency of adenylylsulfate kinase
  • Deficiency of alanine aminotransferase
  • Deficiency of alanine dehydrogenase
  • Deficiency of alanine-oxo-acid aminotransferase
  • Deficiency of alanine-transfer ribonucleic acid ligase
  • Deficiency of alcohol sulfotransferase
  • Deficiency of aldehyde dehydrogenase
  • Deficiency of aldehyde oxidase
  • Deficiency of aldehyde reductase
  • Deficiency of aldehyde-lyase
  • Deficiency of aldonolactonase
  • Deficiency of aldose 1-epimerase
  • Deficiency of alkaline phosphatase
  • Deficiency of alkaline phosphomonoesterase
  • Deficiency of alkylhalidase
  • Deficiency of allantoicase
  • Deficiency of allantoinase
  • Deficiency of alpha- and beta-trypsin
  • Deficiency of alpha-1,4-glucan-protein synthase
  • Deficiency of alpha-aminoacylpeptide hydrolase
  • Deficiency of alpha-amylase
  • Deficiency of alpha-galactosidase
  • Deficiency of alpha-glucosidase
  • Deficiency of amidase
  • Deficiency of amidinotransferase
  • Deficiency of amidophosphoribosyltransferase
  • Deficiency of amine oxidase
  • Deficiency of amine oxidase
  • Deficiency of aminoacyl-histidine dipeptidase
  • Deficiency of aminoacyltransferase
  • Deficiency of aminopeptidase
  • Deficiency of aminotransferase
  • Deficiency of ammonia-lyase
  • Deficiency of amylase
  • Deficiency of amylo-1,6-glucosidase
  • Deficiency of arginine deiminase
  • Deficiency of aromatic-L-amino-acid decarboxylase
  • Deficiency of aryl sulfotransferase
  • Deficiency of arylamine acetyltransferase
  • Deficiency of arylesterase
  • Deficiency of arylsulfatase
  • Deficiency of asparagine-oxo-acid aminotransferase
  • Deficiency of aspartate 4-decarboxylase
  • Deficiency of aspartate aminotransferase
  • Deficiency of aspartate carbamoyltransferase
  • Deficiency of aspartate kinase
  • Deficiency of aspartic proteinase
  • Deficiency of azobenzene reductase
  • Deficiency of benzaldehyde dehydrogenase
  • Deficiency of benzoylcholinesterase
  • Deficiency of beta-amylase
  • Deficiency of beta-fructofuranosidase
  • Deficiency of beta-galactosidase
  • Deficiency of beta-glucosidase
  • Deficiency of beta-glucuronidase
  • Deficiency of betaine-aldehyde dehydrogenase
  • Deficiency of betaine-homocysteine methyltransferase
  • Deficiency of beta-ureidopropionase
  • Deficiency of bisphosphoglycerate mutase
  • Deficiency of bisphosphoglycerate phosphatase
  • Deficiency of butyrate-acetoacetate coenzyme A-transferase
  • Deficiency of butyrylcholine esterase
  • Deficiency of carbamate kinase
  • Deficiency of carbonate dehydratase
  • Deficiency of carbon-carbon lyase
  • Deficiency of carbon-halide lyase
  • Deficiency of carbon-nitrogen lyase
  • Deficiency of carbon-oxygen lyase
  • Deficiency of carbon-sulfur lyase
  • Deficiency of carboxylesterase
  • Deficiency of carboxylic ester hydrolase
  • Deficiency of carboxy-lyase
  • Deficiency of carboxypeptidase A
  • Deficiency of carboxypeptidase B
  • Deficiency of carnitine acetyltransferase
  • Deficiency of carnosinase
  • Deficiency of catalase
  • Deficiency of catechol oxidase
  • Deficiency of cathepsin C
  • Deficiency of cellulase
  • Deficiency of chlorophyllase
  • Deficiency of cholate-CoA ligase
  • Deficiency of cholesterol esterase
  • Deficiency of cholesterol oxidase
  • Deficiency of choline acetyltransferase
  • Deficiency of choline dehydrogenase
  • Deficiency of choline esterase I
  • Deficiency of choline esterase II
  • Deficiency of choline kinase
  • Deficiency of choline-phosphate cytidylyltransferase
  • Deficiency of cholinephosphotransferase
  • Deficiency of cholinesterase
  • Deficiency of chymosin
  • Deficiency of chymotrypsin
  • Deficiency of chymotrypsin A and B
  • Deficiency of citrate
  • Deficiency of coenzyme-A transferase
  • Deficiency of creatine kinase
  • Deficiency of cysteamine dioxygenase
  • Deficiency of cysteine aminotransferase
  • Deficiency of cysteine carboxypeptidase
  • Deficiency of cysteine proteinase
  • Deficiency of cysteinyl-glycine dipeptidase
  • Deficiency of cystine reductase
  • Deficiency of cytidine deaminase
  • Deficiency of cytochrome-b>5< reductase
  • Deficiency of cytochrome-c peroxidase
  • Deficiency of cytosol aminopeptidase
  • Deficiency of D-2-hydroxy-acid dehydrogenase
  • Deficiency of D-amino-acid oxidase
  • Deficiency of D-aspartate oxidase
  • Deficiency of dehydrogenase
  • Deficiency of dehydrogluconate dehydrogenase
  • Deficiency of dehydrogluconokinase
  • Deficiency of deoxyribonuclease I
  • Deficiency of deoxyribonuclease II
  • Deficiency of deoxyribonucleic acid nucleotidylexotransferase
  • Deficiency of deoxyribonucleic acid-directed deoxyribonucleic acid polymerase
  • Deficiency of deoxyribonucleic acid-directed ribonucleic acid polymerase
  • Deficiency of dephospho-coenzyme A kinase
  • Deficiency of dextranase
  • Deficiency of dihydrolipoamide acetyltransferase
  • Deficiency of dihydroorotase
  • Deficiency of dihydrouracil dehydrogenase
  • Deficiency of diisopropyl-fluorophosphatase
  • Deficiency of dimethylallyltranstransferase
  • Deficiency of dioxygenase
  • Deficiency of dipeptidase
  • Deficiency of dipeptide hydrolase
  • Deficiency of dipeptidyl peptidase I
  • Deficiency of dipeptidyl-amino-peptidase I
  • Deficiency of dipeptidylpeptide hydrolase
  • Deficiency of diphosphomevalonate decarboxylase
  • Deficiency of diphosphoric monoester hydrolase
  • Deficiency of D-lactate dehydrogenase
  • Deficiency of endo-1,3
  • Deficiency of endopeptidase
  • Deficiency of endoribonuclease
  • Deficiency of enolase
  • Deficiency of enoyl-coenzyme A hydratase
  • Deficiency of enteropeptidase
  • Deficiency of epimerase
  • Deficiency of erythritol kinase
  • Deficiency of estradiol 6beta-monooxygenase
  • Deficiency of ethanolamine-phosphate cytidylyltransferase
  • Deficiency of ethanolaminephosphotransferase
  • Deficiency of ether hydrolase
  • Deficiency of exoribonuclease
  • Deficiency of ferroxidase
  • Deficiency of formaldehyde dehydrogenase
  • Deficiency of formamidase
  • Deficiency of formate dehydrogenase
  • Deficiency of formate-tetrahydrofolate ligase
  • Deficiency of formiminotetrahydrofolate cyclodeaminase
  • Deficiency of formyltetrahydrofolate deformylase
  • Deficiency of fructose-bisphosphatase
  • Deficiency of fructose-bisphosphate aldolase
  • Deficiency of fumarate hydratase
  • Deficiency of fumarylacetoacetase
  • Deficiency of galactonolactone dehydrogenase
  • Deficiency of galactose dehydrogenase
  • Deficiency of gentisate l,2-dioxygenase
  • Deficiency of glucan 1,3-alpha-glucosidase
  • Deficiency of glucan 1,4-alpha-glucosidase
  • Deficiency of glucokinase
  • Deficiency of gluconate 2-dehydrogenase
  • Deficiency of gluconokinase
  • Deficiency of gluconolactonase
  • Deficiency of glucosamine acetyltransferase
  • Deficiency of glucosamine kinase
  • Deficiency of glucosamine-6-phosphate isomerase
  • Deficiency of glucosamine-phosphate acetyltransferase
  • Deficiency of glucose dehydrogenase
  • Deficiency of glucose oxidase
  • Deficiency of glucose-1-phosphatase
  • Deficiency of glucose-1-phosphate phosphodismutase
  • Deficiency of glucose-6-phosphate dehydrogenase
  • Deficiency of glutamate decarboxylase
  • Deficiency of glutamate dehydrogenase
  • Deficiency of glutamate-ammonia ligase
  • Deficiency of glutaminase
  • Deficiency of glutamine phenylacetyltransferase
  • Deficiency of glutamine-fructose-6-phosphate aminotransferase
  • Deficiency of glutamine-pyruvate aminotransferase
  • Deficiency of glutarate-CoA ligase
  • Deficiency of glutathione reductase
  • Deficiency of glutathione synthase
  • Deficiency of glutathione thiolesterase
  • Deficiency of glutathione-homocystine transhydrogenase
  • Deficiency of glyceraldehyde-3-phosphate dehydrogenase
  • Deficiency of glycerate kinase
  • Deficiency of glycerol kinase
  • Deficiency of glycerol-3-phosphate acyltransferase
  • Deficiency of glycerophosphatase
  • Deficiency of glycerophosphocholine phosphodiesterase
  • Deficiency of glycine acyltransferase
  • Deficiency of glycine amidinotransferase
  • Deficiency of glycine formiminotransferase
  • Deficiency of glycine hydroxymethyltransferase
  • Deficiency of glycosulfatase
  • Deficiency of glycosyltransferase
  • Deficiency of guanidinoacetate kinase
  • Deficiency of guanidinoacetate methyltransferase
  • Deficiency of guanine deaminase
  • Deficiency of guanosine monophosphate synthase
  • Deficiency of heparin lyase
  • Deficiency of hexokinase
  • Deficiency of hexose oxidase
  • Deficiency of hexosyltransferase
  • Deficiency of histidine ammonia-lyase
  • Deficiency of histidine decarboxylase
  • Deficiency of histidinol dehydrogenase
  • Deficiency of homocysteine desulfhydrase
  • Deficiency of homoserine kinase
  • Deficiency of hyaluronate lyase
  • Deficiency of hyaluronoglucosaminidase
  • Deficiency of hydrogen-sulfide acetyltransferase
  • Deficiency of hydrolase
  • Deficiency of hydrolyase
  • Deficiency of hydroxyacylglutathione hydrolase
  • Deficiency of hydroxyalkyl-protein kinase
  • Deficiency of hydroxymethylglutaryl-CoA hydrolase
  • Deficiency of hydroxymethylglutaryl-CoA lyase
  • Deficiency of hydroxymethylglutaryl-coenzyme A reductase
  • Deficiency of hydroxymethylglutaryl-coenzyme A synthase
  • Deficiency of hypoxanthine phosphoribosyltransferase
  • Deficiency of imidodipeptidase
  • Deficiency of iminodipeptidase
  • Deficiency of inorganic pyrophosphatase
  • Deficiency of inosinase
  • Deficiency of inosine monophosphate cyclohydrolase
  • Deficiency of inosine monophosphate dehydrogenase
  • Deficiency of inosine nucleosidase
  • Deficiency of iodide peroxidase
  • Deficiency of isocitrate dehydrogenase
  • Deficiency of isocitrate lyase
  • Deficiency of isoleucine-transfer ribonucleic acid ligase
  • Deficiency of isomerase
  • Deficiency of isopentenyl-diphosphate delta-isomerase
  • Deficiency of ketohexokinase
  • Deficiency of ketotetrose-phosphate aldolase
  • Deficiency of kynurenine 3-monooxygenase
  • Deficiency of kynurenine-oxoglutarate aminotransferase
  • Deficiency of lactate racemase
  • Deficiency of lactonase
  • Deficiency of lactoylglutathione lyase
  • Deficiency of L-amino-acid oxidase
  • Deficiency of L-arabinose dehydrogenase
  • Deficiency of L-asparagine amidohydrolase
  • Deficiency of lecithinase D
  • Deficiency of leucine aminopeptidase
  • Deficiency of leucine aminotransferase
  • Deficiency of leucine-transfer ribonucleic acid ligase
  • Deficiency of L-gulonate dehydrogenase
  • Deficiency of lichenase
  • Deficiency of ligase
  • Deficiency of lipophosphodiesterase II
  • Deficiency of L-lactate dehydrogenase
  • Deficiency of L-lactate dehydrogenase
  • Deficiency of long-chain fatty-acyl-coenzyme A hydrolase
  • Deficiency of long-chain-fatty-acid-CoA ligase
  • Deficiency of L-prolylglycine dipeptidase
  • Deficiency of L-serine dehydratase
  • Deficiency of lyase
  • Deficiency of lysine racemase
  • Deficiency of lysine-transfer ribonucleic acid ligase
  • Deficiency of lysolecithin acylmutase
  • Deficiency of lysophospholipase
  • Deficiency of lysozyme
  • Deficiency of malate dehydrogenase
  • Deficiency of malate dehydrogenase
  • Deficiency of malate dehydrogenase
  • Deficiency of malate oxidase
  • Deficiency of maleylacetoacetate isomerase
  • Deficiency of malonate CoA-transferase
  • Deficiency of malonyl-coenzyme A decarboxylase
  • Deficiency of maltose phosphorylase
  • Deficiency of mannitol dehydrogenase
  • Deficiency of mannokinase
  • Deficiency of mannose-6-phosphate isomerase
  • Deficiency of metallocarboxypeptidase
  • Deficiency of metalloproteinase
  • Deficiency of methenyltetrahydrofolate cyclohydrolase
  • Deficiency of methionine adenosyltransferase
  • Deficiency of methionine-transfer ribonucleic acid ligase
  • Deficiency of methylaspartate mutase
  • Deficiency of methylcrotonoyl-coenzyme A carboxylase
  • Deficiency of methylenetetrahydrofolate dehydrogenase
  • Deficiency of methylglutaconyl-coenzyme A hydratase
  • Deficiency of methylmalonyl-coenzyme A mutase
  • Deficiency of methyltransferase
  • Deficiency of mevaldate reductase
  • Deficiency of mevalonate kinase
  • Deficiency of monodehydroascorbate reductase
  • Deficiency of monooxygenase
  • Deficiency of mutase
  • Deficiency of myo-inositol oxygenase
  • Deficiency of N-acetyl-beta-glucosaminidase
  • Deficiency of N-acetylneuraminate lyase
  • Deficiency of NAPH cytochrome-c>2< reductase
  • Deficiency of nicotinamide adenine dinucleotidase
  • Deficiency of nicotinamide adenine dinucleotide ^+^ kinase
  • Deficiency of nicotinamide adenine dinucleotide ^+^ nucleosidase
  • Deficiency of nicotinamide adenine dinucleotide ^+^ synthase
  • Deficiency of nicotinamide adenine dinucleotide phosphate ^+^ nucleosidase
  • Deficiency of nicotinamide adenine dinucleotide phosphate ^+^ transhydrogenase
  • Deficiency of nicotinamide methyltransferase
  • Deficiency of nicotinamide phosphoribosyltransferase
  • Deficiency of nicotinamide-nucleotide adenylyltransferase
  • Deficiency of nicotinate dehydrogenase
  • Deficiency of nicotinate phosphoribosyltransferase
  • Deficiency of nitrate reductase
  • Deficiency of N-methyl-L-amino-acid oxidase
  • Deficiency of non-specific cholinesterase
  • Deficiency of nucleosidase
  • Deficiency of nucleoside-diphosphatase
  • Deficiency of nucleoside-diphosphate kinase
  • Deficiency of nucleoside-phosphate kinase
  • Deficiency of nucleotidase
  • Deficiency of nucleotide pyrophosphatase
  • Deficiency of nucleotidyltransferase
  • Deficiency of O-acetylserine
  • Deficiency of omega peptidase
  • Deficiency of orotate phosphoribosyltransferase
  • Deficiency of oxalate coenzyme A-transferase
  • Deficiency of oxidase
  • Deficiency of oximinotransferase
  • Deficiency of oxo-acid-lyase
  • Deficiency of oxoglutarate dehydrogenase
  • Deficiency of oxygenase
  • Deficiency of palmitoyl-coenzyme A hydrolase
  • Deficiency of pancreatic elastase
  • Deficiency of pantetheine kinase
  • Deficiency of pantetheine-phosphate adenylyltransferase
  • Deficiency of pantothenoylcysteine decarboxylase
  • Deficiency of pectin methoxylase
  • Deficiency of pectin methylesterase
  • Deficiency of pectinesterase
  • Deficiency of pentosyltransferase
  • Deficiency of pepsin A
  • Deficiency of pepsin B
  • Deficiency of peptidase a
  • Deficiency of peptide hydrolase
  • Deficiency of peptidoglycan endopeptidase
  • Deficiency of peroxidase
  • Deficiency of phenylalanine 4-monooxygenase
  • Deficiency of phenylpyruvate tautomerase
  • Deficiency of phosphatase
  • Deficiency of phosphatidate phosphatase
  • Deficiency of phosphoacetylglucosamine mutase
  • Deficiency of phosphoadenylate 3'-nucleotidase
  • Deficiency of phosphoamidase
  • Deficiency of phosphoglucokinase
  • Deficiency of phosphogluconate dehydrogenase
  • Deficiency of phosphogluconate dehydrogenase
  • Deficiency of phosphoglycerate kinase
  • Deficiency of phosphoglycerate mutase
  • Deficiency of phosphoketolase
  • Deficiency of phospholipase A>2<
  • Deficiency of phospholipase C
  • Deficiency of phospholipase D
  • Deficiency of phosphomevalonate kinase
  • Deficiency of phosphomonoesterase
  • Deficiency of phosphopantothenate-cysteine ligase
  • Deficiency of phosphoprotein phosphatase
  • Deficiency of phosphoribokinase
  • Deficiency of phosphoribosylamine-glycine ligase
  • Deficiency of phosphoribosylaminoimidazole carboxylase
  • Deficiency of phosphoribosylaminoimidazolecarboxamide formyltransferase
  • Deficiency of phosphoribosylaminoimidazole-succinocarboxamide synthase
  • Deficiency of phosphoribosylformylglycinamidine cyclo-ligase
  • Deficiency of phosphoribosylformylglycinamidine synthase
  • Deficiency of phosphoribosylglycinamide formyltransferase
  • Deficiency of phosphoric diester hydrolase
  • Deficiency of phosphoric monoester hydrolase
  • Deficiency of phosphorus-oxygen lyase
  • Deficiency of phosphorylase phosphatase
  • Deficiency of phosphoserine phosphatase
  • Deficiency of phosphotransferase
  • Deficiency of plasmin
  • Deficiency of polygalacturonase
  • Deficiency of polyribonucleotide nucleotidyltransferase
  • Deficiency of progesterone 11alpha-monooxygenase
  • Deficiency of prolidase
  • Deficiency of prolinase
  • Deficiency of proline dipeptidase
  • Deficiency of prolyl dipeptidase
  • Deficiency of propionyl-coenzyme A carboxylase
  • Deficiency of protein kinase
  • Deficiency of protocatechuate 3,4-dioxygenase
  • Deficiency of pyridoxal kinase
  • Deficiency of pyridoxamine-phosphate oxidase
  • Deficiency of pyrophosphotransferase
  • Deficiency of pyrroline-2-carboxylate reductase
  • Deficiency of pyrroline-5-carboxylate reductase
  • Deficiency of pyruvate decarboxylase
  • Deficiency of quinate dehydrogenase
  • Deficiency of racemase
  • Deficiency of reduced nicotinamide adenine dinucleotide dehydrogenase
  • Deficiency of reduced nicotinamide adenine dinucleotide phosphate dehydrogenase
  • Deficiency of reduced nicotinamide adenine dinucleotide phosphate-ferrihemoprotein reductase
  • Deficiency of reductase
  • Deficiency of renin
  • Deficiency of retinal isomerase
  • Deficiency of retinyl-palmitate esterase
  • Deficiency of rhamnulokinase
  • Deficiency of riboflavin kinase
  • Deficiency of riboflavin mononucleotide adenylyltransferase
  • Deficiency of ribokinase
  • Deficiency of ribonuclease
  • Deficiency of ribose-5-phosphate isomerase
  • Deficiency of ribose-phosphate pyrophosphokinase
  • Deficiency of ribosomal cathepsin
  • Deficiency of ribosomal neutral proteinase
  • Deficiency of ribosylnicotinamide kinase
  • Deficiency of ribulokinase
  • Deficiency of ribulose-phosphate 3-epimerase
  • Deficiency of sarcosine oxidase
  • Deficiency of sedoheptulokinase
  • Deficiency of serine carboxypeptidase
  • Deficiency of serine proteinase
  • Deficiency of serine-transfer ribonucleic acid ligase
  • Deficiency of shikimate dehydrogenase
  • Deficiency of sialidase
  • Deficiency of squalene monooxygenase
  • Deficiency of steroid 11-beta-monooxygenase
  • Deficiency of steroid 17-alpha-monooxygenase
  • Deficiency of steroid 21-monooxygenase
  • Deficiency of steroid delta-isomerase
  • Deficiency of succinate- coenzyme A ligase
  • Deficiency of succinate dehydrogenase
  • Deficiency of succinate-coenzyme A ligase
  • Deficiency of succinate-coenzyme A ligase
  • Deficiency of succinyl-coenzyme A hydrolase
  • Deficiency of sulfatase
  • Deficiency of sulfate adenylyltransferase
  • Deficiency of sulfinoalanine decarboxylase
  • Deficiency of sulfite reductase
  • Deficiency of sulfotransferase
  • Deficiency of sulfuric ester hydrolase
  • Deficiency of sulfurtransferase
  • Deficiency of tannase
  • Deficiency of thetin-homocysteine methyltransferase
  • Deficiency of thiamin pyridinylase
  • Deficiency of thiamin pyrophosphokinase
  • Deficiency of thioethanolamine acetyltransferase
  • Deficiency of thioether hydrolase
  • Deficiency of thiolester hydrolase
  • Deficiency of thiosulfate sulfurtransferase
  • Deficiency of threonine aldolase
  • Deficiency of threonine dehydratase
  • Deficiency of threonine-transfer ribonucleic acid ligase
  • Deficiency of thymidine phosphorylase
  • Deficiency of transacylase
  • Deficiency of transaldolase
  • Deficiency of transcarbamoylase
  • Deficiency of transcarboxylase
  • Deficiency of transferase
  • Deficiency of transformiminase
  • Deficiency of transformylase
  • Deficiency of transhydroxymethylase
  • Deficiency of transketolase
  • Deficiency of triacylglycerol lipase
  • Deficiency of trimetaphosphatase
  • Deficiency of triokinase
  • Deficiency of tripeptide aminopeptidase
  • Deficiency of triphosphoric monoester hydrolase
  • Deficiency of tropinesterase
  • Deficiency of true cholinesterase
  • Deficiency of trypsin
  • Deficiency of tryptophan 2,3-dioxygenase
  • Deficiency of tryptophan 5-monooxygenase
  • Deficiency of tryptophan-transfer ribonucleic acid ligase
  • Deficiency of tyraminase
  • Deficiency of tyrosine aminotransferase
  • Deficiency of tyrosine decarboxylase
  • Deficiency of tyrosine-transfer ribonucleic acid ligase
  • Deficiency of unspecific monooxygenase
  • Deficiency of uracil dehydrogenase
  • Deficiency of uracil phosphoribosyltransferase
  • Deficiency of urate oxidase
  • Deficiency of urease
  • Deficiency of uridine diphosphate-glucose dehydrogenase
  • Deficiency of uridine diphosphate-glucose-hexose-1-phosphate uridylyltransferase
  • Deficiency of uridine phosphorylase
  • Deficiency of uridine triphosphate-glucose-1-phosphate uridylyltransferase
  • Deficiency of uronolactonase
  • Deficiency of valine-transfer ribonucleic acid ligase
  • Deficiency of w-amidase
  • Deficiency of xanthine oxidase
  • Deficiency of xylan endo-1,3-beta-xylosidase
  • Deficiency of xylulokinase
  • Disorder involving deficiency of steryl-sulfatase
  • Glycerol kinase deficiency - contiguous gene syndrome
  • Hereditary angioedema
  • Hereditary angioedema with normal C1 esterase inhibitor activity
  • Metachromatic leukodystrophy due to deficiency of cerebroside sulfatase activator
  • Muscle L-lactate dehydrogenase deficiency
  • Pancreatic alpha-amylase deficiency
  • Phosphoglycerokinase deficiency
  • Specific enzyme deficiency
  • Succinate-coenzyme Q reductase deficiency
  • Ubiquinone dehydrogenase

References to Index of Diseases and Injuries

The code 277.6 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Angioedema (allergic) (any site) (with urticaria) 995.1
    • hereditary 277.6
  • Angioneurotic edema (allergic) (any site) (with urticaria) 995.1
    • hereditary 277.6
  • Deficiency, deficient
    • biotinidase 277.6
    • bradykinase-1 277.6
    • dihydropyrimidine dehydrogenase (DPD) 277.6
    • enzymes, circulating NEC (see also Deficiency, by specific enzyme) 277.6
  • Dihydropyrimidine dehydrogenase disease (DPD) 277.6
  • DPD (dihydropyrimidine dehydrogenase deficiency) 277.6
  • Edema, edematous 782.3
    • angioneurotic (allergic) (any site) (with urticaria) 995.1
      • hereditary 277.6
    • circumscribed, acute 995.1
      • hereditary 277.6
    • essential, acute 995.1
      • hereditary 277.6
    • glottis, glottic, glottides (obstructive) (passive) 478.6
      • allergic 995.1
        • hereditary 277.6
    • periodic 995.1
      • hereditary 277.6
    • Quincke's 995.1
      • hereditary 277.6
  • Giant
    • urticaria 995.1
      • hereditary 277.6
  • Opisthognathism 524.00
  • Periodic - see also condition
    • edema 995.1
      • hereditary 277.6
  • Urticaria 708.9
    • with angioneurotic edema 995.1
      • hereditary 277.6
    • giant 995.1
      • hereditary 277.6
    • gigantea 995.1
      • hereditary 277.6
    • larynx 995.1
      • hereditary 277.6

Crosswalk Information

The code 277.6 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
277.6 Right Arrow D84.1 Defects in the complement system
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
277.00 Cystic fibrosis without mention of meconium ileus
277.01 Cystic fibrosis with meconium ileus
277.02 Cystic fibrosis with pulmonary manifestations
277.03 Cystic fibrosis with gastrointestinal manifestations
277.09 Cystic fibrosis with other manifestations
277.1 Disorders of porphyrin metabolism
277.2 Other disorders of purine and pyrimidine metabolism
277.30 Amyloidosis, unspecified
277.31 Familial Mediterranean fever
277.39 Other amyloidosis
277.4 Disorders of bilirubin excretion
277.5 Mucopolysaccharidosis
277.7 Dysmetabolic syndrome X
277.81 Primary carnitine deficiency
277.82 Carnitine deficiency due to inborn errors of metabolism
277.83 Iatrogenic carnitine deficiency
277.84 Other secondary carnitine deficiency
277.85 Disorders of fatty acid oxidation
277.86 Peroxisomal disorders
277.87 Disorders of mitochondrial metabolism
277.88 Tumor lysis syndrome
277.89 Other specified disorders of metabolism
277.9 Unspecified disorder of metabolism


This page was last updated on: 10/1/2014