282.3 ENZYME DEFIC ANEMIA NEC


Code Information

Diagnosis Code: 282.3

Short Description: Enzyme defic anemia NEC

Long Description: Other hemolytic anemias due to enzyme deficiency

Code Classification:

  • Diseases of the blood and blood-forming organs (280–289)
    • Diseases of the blood and blood-forming organs (280-289)
      • 282 Hereditary hemolytic anemias
        • 282.3 Enzyme defic anemia NEC

Code Version: 2015 ICD-9-CM


Synonyms

  • Anemia due to enzyme deficiency
  • Chronic non-spherocytic hemolytic anemia
  • Deficiency of pyruvate kinase
  • Fumarase deficiency
  • Hemolytic anemia due to hexokinase deficiency
  • Hemolytic anemia due to pyruvate kinase deficiency
  • Hemolytic anemia due to triose phosphate isomerase deficiency
  • Hereditary nonspherocytic hemolytic anemia
  • Hereditary nonspherocytic hemolytic anemia due to aldolase A deficiency
  • Hereditary nonspherocytic hemolytic anemia due to decreased adenosine deaminase activity
  • Hereditary nonspherocytic hemolytic anemia due to diphosphoglycerate mutase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to gamma glutamyl cysteine synthetase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to glucose phosphate isomerase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to hexokinase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to increased adenosine deaminase activity
  • Hereditary nonspherocytic hemolytic anemia due to phosphofructokinase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to phosphoglycerate kinase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to pyrimidine-5'-nucleotidase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to pyruvate kinase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to reduced nicotinamide adenine dinucleotide diaphorase deficiency
  • Hereditary nonspherocytic hemolytic anemia due to triosephosphate isomerase deficiency
  • Triose phosphate isomerase deficiency

References to Index of Diseases and Injuries

The code 282.3 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Anemia 285.9
    • with
      • disorder of
        • anaerobic glycolysis 282.3
    • congenital (following fetal blood loss) 776.5
      • nonspherocytic
        • type II 282.3
    • Dacie's (nonspherocytic)
      • type II 282.3
    • deficiency 281.9
      • 2, 3 diphosphoglycurate mutase 282.3
      • 2, 3 PG 282.3
      • glucose-phosphate isomerase 282.3
      • glyceraldehyde phosphate dehydrogenase 282.3
      • GPI 282.3
      • hexokinase 282.3
      • PFK 282.3
      • phosphofructo-aldolase 282.3
      • phosphofructokinase 282.3
      • phosphoglycerate kinase 282.3
      • PK 282.3
      • pyruvate kinase (PK) 282.3
      • TPI 282.3
      • triosephosphate isomerase 282.3
    • due to
      • defect of Embden-Meyerhof pathway glycolysis 282.3
    • hemolytic 283.9
      • acute 283.9
        • due to enzyme deficiency NEC 282.3
      • due to
        • enzyme deficiency NEC 282.3
          • drug-induced 282.2
      • hereditary 282.9
        • due to enzyme deficiency NEC 282.3
      • nonspherocytic
        • congenital or hereditary NEC 282.3
          • glucose-6-phosphate dehydrogenase deficiency 282.2
          • pyruvate kinase (PK) deficiency 282.3
          • type I 282.2
          • type II 282.3
        • type II 282.3
    • hexokinase deficiency 282.3
    • pyruvate kinase (PK) deficiency 282.3
    • triosephosphate isomerase deficiency 282.3
  • Deficiency, deficient
    • pyruvate kinase (PK) 282.3
  • Disorder - see also Disease
    • anaerobic glycolysis with anemia 282.3
  • Maldescent, testis 752.51
  • Metalliferous miners' lung 503
  • Microgenitalia (congenital) 752.89

Crosswalk Information

The code 282.3 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
282.3 Right Arrow D55.8 Other anemias due to enzyme disorders
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
282.0 Hereditary spherocytosis
282.1 Hereditary elliptocytosis
282.2 Anemias due to disorders of glutathione metabolism
282.40 Thalassemia, unspecified
282.41 Sickle-cell thalassemia without crisis
282.42 Sickle-cell thalassemia with crisis
282.43 Alpha thalassemia
282.44 Beta thalassemia
282.45 Delta-beta thalassemia
282.46 Thalassemia minor
282.47 Hemoglobin E-beta thalassemia
282.49 Other thalassemia
282.5 Sickle-cell trait
282.60 Sickle-cell disease, unspecified
282.61 Hb-SS disease without crisis
282.62 Hb-SS disease with crisis
282.63 Sickle-cell/Hb-C disease without crisis
282.64 Sickle-cell/Hb-C disease with crisis
282.68 Other sickle-cell disease without crisis
282.69 Other sickle-cell disease with crisis
282.7 Other hemoglobinopathies
282.8 Other specified hereditary hemolytic anemias
282.9 Hereditary hemolytic anemia, unspecified


This page was last updated on: 10/1/2014