283.2 HEMOLYTIC HEMOGLOBINURIA


Code Information

Diagnosis Code: 283.2

Short Description: Hemolytic hemoglobinuria

Long Description: Hemoglobinuria due to hemolysis from external causes

Code Classification:

  • Diseases of the blood and blood-forming organs (280–289)
    • Diseases of the blood and blood-forming organs (280-289)
      • 283 Acquired hemolytic anemias
        • 283.2 Hemolytic hemoglobinuria

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 283.2 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Anemia 285.9
    • hemolytic 283.9
      • acquired 283.9
        • with hemoglobinuria NEC 283.2
  • Cold 460
    • agglutinin
      • hemoglobinuria 283.0
        • paroxysmal (cold) (nocturnal) 283.2
  • Disease, diseased - see also Syndrome
    • cold
      • agglutinin 283.0
        • or hemoglobinuria 283.0
          • paroxysmal (cold) (nocturnal) 283.2
    • Harley's (intermittent hemoglobinuria) 283.2
    • Murri's (intermittent hemoglobinuria) 283.2
  • Harley's disease (intermittent hemoglobinuria) 283.2
  • Hematinuria (see also Hemoglobinuria) 791.2
    • paroxysmal 283.2
  • Hemoglobinemia 283.2
    • due to blood transfusion NEC 999.89
      • bone marrow 996.85
    • paroxysmal 283.2
  • Hemoglobinuria, hemoglobinuric 791.2
    • with anemia, hemolytic, acquired (chronic) NEC 283.2
    • cold (agglutinin) (paroxysmal) (with Raynaud's syndrome) 283.2
    • due to
      • exertion 283.2
      • hemolysis (from external causes) NEC 283.2
    • exercise 283.2
    • intermittent 283.2
    • march 283.2
    • nocturnal (paroxysmal) 283.2
    • paroxysmal (cold) (nocturnal) 283.2
  • Hemolysis
    • intravascular (disseminated) NEC 286.6
      • acute 283.2
  • March
    • hemoglobinuria 283.2
  • Marchiafava-Micheli syndrome (paroxysmal nocturnal hemoglobinuria) 283.2
  • Murri's disease (intermittent hemoglobinuria) 283.2
  • Syndrome - see also Disease
    • Dressler's (postmyocardial infarction) 411.0
      • hemoglobinuria 283.2
    • Marchiafava-Micheli (paroxysmal nocturnal hemoglobinuria) 283.2

Crosswalk Information

The code 283.2 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
283.2 Right Arrow D59.5 Paroxysmal nocturnal hemoglobinuria [Marchiafava-Micheli]
D59.6 Hemoglobinuria due to hemolysis from other external causes
D59.8 Other acquired hemolytic anemias
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
283.0 Autoimmune hemolytic anemias
283.10 Non-autoimmune hemolytic anemia, unspecified
283.11 Hemolytic-uremic syndrome
283.19 Other non-autoimmune hemolytic anemias
283.9 Acquired hemolytic anemia, unspecified


This page was last updated on: 10/1/2014