330.0 LEUKODYSTROPHY


Code Information

Diagnosis Code: 330.0

Short Description: Leukodystrophy

Long Description: Leukodystrophy

Code Classification:

  • Diseases of the nervous system (320–359)
    • Hereditary and degenerative diseases of the central nervous system (330-337)
      • 330 Cerebral degenerations usually manifest in childhood
        • 330.0 Leukodystrophy

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 330.0 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Aplasia - see also Agenesis
    • axialis extracorticalis (congenital) 330.0
    • extracortical axial 330.0
    • Pelizaeus-Merzbacher 330.0
  • Canavan's disease 330.0
  • Disease, diseased - see also Syndrome
    • Canavan's 330.0
    • Greenfield's 330.0
    • Krabbe's 330.0
    • Merzbacher-Pelizaeus 330.0
    • Pelizaeus-Merzbacher 330.0
      • with dementia
        • with behavioral disturbance 330.0 [294.11]
        • without behavioral disturbance 330.0 [294.10]
    • Scholz's 330.0
    • van Bogaert-Nijssen (-Peiffer) 330.0
  • Encephalopathy (acute) 348.30
    • leukopolio 330.0
  • Greenfield's disease 330.0
  • Krabbe's
    • disease (leukodystrophy) 330.0
  • Leukodystrophy (cerebral) (globoid cell) (metachromatic) (progressive) (sudanophilic) 330.0
  • Leukoencephalopathy (see also Encephalitis) 323.9
    • metachromatic 330.0
  • Leukopolioencephalopathy 330.0
  • Lipidosis 272.7
    • sulfatide 330.0
  • Merzbacher-Pelizaeus disease 330.0
  • Myeloleukodystrophy 330.0
  • Pelizaeus-Merzbacher
    • disease 330.0
    • sclerosis, diffuse cerebral 330.0
  • Scholz's disease 330.0
  • Scholz (-Bielschowsky-Henneberg) syndrome 330.0
  • Sclerosis, sclerotic
    • brain (general) (lobular) 348.89
      • diffuse 341.1
        • familial (chronic) (infantile) 330.0
        • infantile (chronic) (familial) 330.0
        • Pelizaeus-Merzbacher type 330.0
      • infantile (degenerative) (diffuse) 330.0
      • Krabbe's 330.0
      • Pelizaeus-Merzbacher 330.0
      • progressive familial 330.0
    • centrolobar, familial 330.0
  • Sulfatidosis 330.0
  • Syndrome - see also Disease
    • retroviral seroconversion (acute) V08
    • Scholz (-Bielschowsky-Henneberg) 330.0
  • van Bogaert-Nijssen (-Peiffer) disease 330.0

Crosswalk Information

The code 330.0 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
330.0 Right Arrow E75.23 Krabbe disease
E75.25 Metachromatic leukodystrophy
E75.29 Other sphingolipidosis
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
330.1 Cerebral lipidoses
330.2 Cerebral degeneration in generalized lipidoses
330.3 Cerebral degeneration of childhood in other diseases classified elsewhere
330.8 Other specified cerebral degenerations in childhood
330.9 Unspecified cerebral degeneration in childhood


This page was last updated on: 10/1/2014