416.0 PRIM PULM HYPERTENSION


Code Information

Diagnosis Code: 416.0

Short Description: Prim pulm hypertension

Long Description: Primary pulmonary hypertension

Code Classification:

  • Diseases of the circulatory system (390–459)
    • Diseases of pulmonary circulation (415-417)
      • 416 Chronic pulmonary heart disease
        • 416.0 Prim pulm hypertension

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 416.0 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Arrillaga-Ayerza syndrome (pulmonary artery sclerosis with pulmonary hypertension) 416.0
  • Arteriosclerosis, arteriosclerotic (artery) (deformans) (diffuse) (disease) (endarteritis) (general) (obliterans) (obliterative) (occlusive) (senile) (with calcification) 440.9
    • pulmonary (idiopathic) 416.0
  • Ayerza's disease or syndrome (pulmonary artery sclerosis with pulmonary hypertension) 416.0
  • Cardiopathia nigra 416.0
  • Disease, diseased - see also Syndrome
    • Ayerza's (pulmonary artery sclerosis with pulmonary hypertension) 416.0
    • heart (organic) 429.9
      • black 416.0
    • pulmonary - see also Disease, lung
      • hypertensive (vascular) 416.0
        • cardiovascular 416.0
  • Hypertension, hypertensive (arterial) (arteriolar) (crisis) (degeneration) (disease) (essential) (fluctuating) (idiopathic) (intermittent) (labile) (low renin) (orthostatic) (paroxysmal) (primary) (systemic) (uncontrolled) (vascular).......................................... 401.0......... 401.1......... 401.9
    • lesser circulation..................................................................... -................ -............ 416.0
    • pulmonary (artery) (secondary)������ ...................................... -................ -............ 416.8
      • idiopathic......................................................................................................... 416.0
      • primary............................................................................................................. 416.0
        • of newborn................................................................................................. 747.83
  • Sclerosis, sclerotic
    • pulmonary (see also Fibrosis, lung) 515
      • artery 416.0
  • Syndrome - see also Disease
    • Arrillaga-Ayerza (pulmonary artery sclerosis with pulmonary hypertension) 416.0
    • Ayerza (-Arrillaga) (pulmonary artery sclerosis with pulmonary hypertension) 416.0
    • cardiacos negros 416.0
    • pulmonary
      • arteriosclerosis 416.0

Crosswalk Information

The code 416.0 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
416.0 Right Arrow I27.0 Primary pulmonary hypertension
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
416.1 Kyphoscoliotic heart disease
416.2 Chronic pulmonary embolism
416.8 Other chronic pulmonary heart diseases
416.9 Chronic pulmonary heart disease, unspecified


This page was last updated on: 10/1/2014