E77.0 DEFECTS IN POST-TRANSLATIONAL MOD OF LYSOSOMAL ENZYMES

Code Information

  • Diagnosis Code: E77.0
  • Short Description: Defects in post-translational mod of lysosomal enzymes
  • Long Description: Defects in post-translational modification of lysosomal enzymes
  • Code Version: 2025 ICD-10-CM

The code E77.0 is VALID for claim submission

Code Classification

Synonyms

  • Defect in post-translational modification of lysosomal enzymes
  • I-cell disease
  • Mucolipidosis
  • Mucolipidosis
  • Pseudo-Hurler polydystrophy

References to Index of Diseases and Injuries

The code E77.0 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Mucolipidosis II [I-cell disease]
    • Mucolipidosis III [pseudo-Hurler polydystrophy]

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E77.0 Right Arrow 272.7 Lipidoses
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E77 Disorders of glycoprotein metabolism
E77.1 Defects in glycoprotein degradation
E77.8 Other disorders of glycoprotein metabolism
E77.9 Disorder of glycoprotein metabolism, unspecified
This page was last updated on: 10/1/2025
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