E78.3 HYPERCHYLOMICRONEMIA

Code Information

  • Diagnosis Code: E78.3
  • Short Description: Hyperchylomicronemia
  • Long Description: Hyperchylomicronemia
  • Code Version: 2025 ICD-10-CM

The code E78.3 is VALID for claim submission

Code Classification

Synonyms

  • Chylomicron retention disease
  • Chylomicronemia syndrome
  • Endogenous hyperlipidemia
  • Endogenous hyperlipidemia
  • Endogenous hyperlipidemia
  • Endogenous hyperlipidemia
  • Familial apolipoprotein C-II deficiency
  • Familial chylomicronemia syndrome
  • Familial hyperchylomicronemia
  • Familial hypertriglyceridemia
  • Familial hypertriglyceridemia
  • Familial hypertriglyceridemia
  • Familial hypertriglyceridemia
  • Familial lipoprotein lipase deficiency with type I phenotype
  • Familial lipoprotein lipase deficiency with type V phenotype
  • Familial type 5 hyperlipoproteinemia
  • Hyperlipidemia with lipid deposition in skin
  • Hyperlipidemia with lipid deposition in skin
  • Hyperlipidemia with lipid deposition in skin
  • Hyperlipidemia with lipid deposition in skin
  • Hyperlipidemia with lipid deposition in skin
  • Hyperlipidemia with lipid deposition in skin
  • Hyperlipidemia with lipid deposition in skin
  • Hyperlipoproteinemia
  • Hyperlipoproteinemia, type I
  • Lipidemia retinalis
  • Primary acquired chylomicronemia
  • Primary chylomicronemia
  • Primary genetic hyperlipidemia
  • Primary genetic hyperlipidemia
  • Primary genetic hyperlipidemia
  • Primary genetic hyperlipidemia
  • Primary hypertriglyceridemia
  • Primary hypertriglyceridemia
  • Primary hypertriglyceridemia
  • Primary hypertriglyceridemia
  • Xanthoma due to abnormality of lipid metabolism
  • Xanthoma due to primary chylomicronemia

References to Index of Diseases and Injuries

The code E78.3 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Chylomicron retention disease
    • Fredrickson's hyperlipoproteinemia, type I or V
    • Hyperlipidemia, group D
    • Mixed hyperglyceridemia

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E78.3 Right Arrow 272.3 Hyperchylomicronemia
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E78 Disorders of lipoprotein metabolism and other lipidemias
E78.0 Pure hypercholesterolemia
E78.00 Pure hypercholesterolemia, unspecified
E78.01 Familial hypercholesterolemia
E78.1 Pure hyperglyceridemia
E78.2 Mixed hyperlipidemia
E78.4 Other hyperlipidemia
E78.41 Elevated Lipoprotein(a)
E78.49 Other hyperlipidemia
E78.5 Hyperlipidemia, unspecified
E78.6 Lipoprotein deficiency
E78.7 Disorders of bile acid and cholesterol metabolism
E78.70 Disorder of bile acid and cholesterol metabolism, unspecified
E78.71 Barth syndrome
E78.72 Smith-Lemli-Opitz syndrome
E78.79 Other disorders of bile acid and cholesterol metabolism
E78.8 Other disorders of lipoprotein metabolism
E78.81 Lipoid dermatoarthritis
E78.89 Other lipoprotein metabolism disorders
E78.9 Disorder of lipoprotein metabolism, unspecified
This page was last updated on: 10/1/2024
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