E88.43 DISORDERS OF MITOCHONDRIAL TRNA SYNTHETASES

Code Information

  • Diagnosis Code: E88.43
  • Short Description: Disorders of mitochondrial tRNA synthetases
  • Long Description: Disorders of mitochondrial tRNA synthetases
  • Code Version: 2025 ICD-10-CM

The code E88.43 is VALID for claim submission

Code Classification

References to Index of Diseases and Injuries

The code E88.43 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • ARS2-related mitochondrial disorders
    • LBSL
    • Leukoencephalopathy with brainstem - spinal cord involvement - lactate elevation
    • Leukoencephalopathy with thalamus - brainstem involvement - high lactate
    • LTBL
    • Mitochondrial aminoacyl-tRNA synthetase disorders
  • Code Also:
    • , if applicable, associated condition such as:
    • leukoencephalopathy (@G93.49*)

Similar Codes

ICD-10 Code ICD-10 Description
E88 Other and unspecified metabolic disorders
E88.0 Disorders of plasma-protein metabolism, not elsewhere classified
E88.01 Alpha-1-antitrypsin deficiency
E88.02 Plasminogen deficiency
E88.09 Other disorders of plasma-protein metabolism, not elsewhere classified
E88.1 Lipodystrophy, not elsewhere classified
E88.10 Lipodystrophy, unspecified
E88.11 Partial lipodystrophy
E88.12 Generalized lipodystrophy
E88.13 Localized lipodystrophy
E88.14 HIV-associated lipodystrophy
E88.19 Other lipodystrophy, not elsewhere classified
E88.2 Lipomatosis, not elsewhere classified
E88.3 Tumor lysis syndrome
E88.4 Mitochondrial metabolism disorders
E88.40 Mitochondrial metabolism disorder, unspecified
E88.41 MELAS syndrome
E88.42 MERRF syndrome
E88.49 Other mitochondrial metabolism disorders
E88.8 Other specified metabolic disorders
E88.81 Metabolic syndrome and other insulin resistance
E88.810 Metabolic syndrome
E88.811 Insulin resistance syndrome, Type A
E88.818 Other insulin resistance
E88.819 Insulin resistance, unspecified
E88.82 Obesity due to disruption of MC4R pathway
E88.89 Other specified metabolic disorders
E88.9 Metabolic disorder, unspecified
E88.A Wasting disease (syndrome) due to underlying condition
This page was last updated on: 10/1/2025