Diagnosis Code

H47.22 HEREDITARY OPTIC ATROPHY


Code Information

Diagnosis Code: H47.22

Short Description: Hereditary optic atrophy

Long Description: Hereditary optic atrophy

The code H47.22 is VALID for claim submission

Code Classification:

  • Diseases of the eye and adnexa (H00–H59)
    • Disorders of optic nerve and visual pathways (H46-H47)
      • Other disorders of optic [2nd] nerve and visual pathways (H47)
        • H47.22 Hereditary optic atrophy

Code Version: 2022 ICD-10-CM


Synonyms

  • Absence of teeth
  • Auditory neuropathy, optic atrophy syndrome
  • Autosomal dominant optic atrophy and cataract
  • Autosomal dominant optic atrophy and peripheral neuropathy syndrome
  • Autosomal dominant optic atrophy classic form
  • Autosomal dominant optic atrophy plus syndrome
  • Autosomal recessive bilateral optic atrophy
  • Autosomal recessive isolated optic atrophy
  • Autosomal recessive optic atrophy type 6
  • Autosomal recessive optic atrophy type 7
  • Autosomal recessive spastic ataxia, optic atrophy, dysarthria syndrome
  • Axonal neuropathy
  • Bilateral optic atrophy of eyes
  • Bilateral optic atrophy of eyes
  • Bilateral optic atrophy of eyes
  • Bilateral primary optic atrophy
  • Bilateral primary optic atrophy
  • CAMOS syndrome
  • Cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss syndrome
  • Childhood-onset autosomal dominant optic atrophy
  • Congenital atrophy of optic nerve
  • Congenital atrophy of optic nerve
  • Congenital atrophy of optic nerve
  • Congenital atrophy of optic nerve
  • Congenital atrophy of optic nerve
  • Dominant hereditary optic atrophy
  • Dominant hereditary optic atrophy
  • Dominant hereditary optic atrophy
  • Dominant hereditary optic atrophy
  • Early-onset progressive diffuse brain atrophy, microcephaly, muscle weakness, optic atrophy syndrome
  • Early-onset X-linked optic atrophy
  • False anodontia
  • GAPO syndrome
  • Generalized dystonia
  • Genetic anomaly of leukocyte
  • Hereditary bilateral optic atrophy
  • Hereditary left optic atrophy
  • Hereditary motor and sensory neuropathy with optic atrophy
  • Hereditary optic atrophy
  • Hereditary right optic atrophy
  • Infantile-onset axonal motor and sensory neuropathy, optic atrophy, neurodegenerative syndrome
  • Leber plus disease
  • Leber's optic atrophy
  • Maternally inherited mitochondrial deoxyribonucleic acid disease
  • Maternally inherited mitochondrial deoxyribonucleic acid disease
  • MEPAN syndrome
  • Optic atrophy, ataxia, peripheral neuropathy, global developmental delay syndrome
  • Optic atrophy, intellectual disability syndrome
  • Pelger-Huët anomaly
  • Pelger-Huët cell
  • Second cranial nerve finding
  • Second cranial nerve finding
  • Second cranial nerve finding
  • Second cranial nerve finding
  • Severe X-linked intellectual disability Gustavson type
  • Short stature, optic nerve atrophy, Pelger-Huët anomaly syndrome
  • Spastic paraplegia, optic atrophy, neuropathy syndrome
  • SPOAN and SPOAN-related disorder
  • SPOAN and SPOAN-related disorder
  • Tooth absent
  • X-linked optic atrophy

References to Index of Diseases and Injuries

The code H47.22 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Leber's optic atrophy

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
H47.22 Right Arrow 377.16 Hereditary optic atrophy

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
H47 Other disorders of optic [2nd] nerve and visual pathways
H47.0 Disorders of optic nerve, not elsewhere classified
H47.01 Ischemic optic neuropathy
H47.011 Ischemic optic neuropathy, right eye
H47.012 Ischemic optic neuropathy, left eye
H47.013 Ischemic optic neuropathy, bilateral
H47.019 Ischemic optic neuropathy, unspecified eye
H47.02 Hemorrhage in optic nerve sheath
H47.021 Hemorrhage in optic nerve sheath, right eye
H47.022 Hemorrhage in optic nerve sheath, left eye
H47.023 Hemorrhage in optic nerve sheath, bilateral
H47.029 Hemorrhage in optic nerve sheath, unspecified eye
H47.03 Optic nerve hypoplasia
H47.031 Optic nerve hypoplasia, right eye
H47.032 Optic nerve hypoplasia, left eye
H47.033 Optic nerve hypoplasia, bilateral
H47.039 Optic nerve hypoplasia, unspecified eye
H47.09 Other disorders of optic nerve, not elsewhere classified
H47.091 Other disorders of optic nerve, not elsewhere classified, right eye
H47.092 Other disorders of optic nerve, not elsewhere classified, left eye
H47.093 Other disorders of optic nerve, not elsewhere classified, bilateral
H47.099 Other disorders of optic nerve, not elsewhere classified, unspecified eye
H47.1 Papilledema
H47.10 Unspecified papilledema
H47.11 Papilledema associated with increased intracranial pressure
H47.12 Papilledema associated with decreased ocular pressure
H47.13 Papilledema associated with retinal disorder
H47.14 Foster-Kennedy syndrome
H47.141 Foster-Kennedy syndrome, right eye
H47.142 Foster-Kennedy syndrome, left eye
H47.143 Foster-Kennedy syndrome, bilateral
H47.149 Foster-Kennedy syndrome, unspecified eye
H47.2 Optic atrophy
H47.20 Unspecified optic atrophy
H47.21 Primary optic atrophy
H47.211 Primary optic atrophy, right eye
H47.212 Primary optic atrophy, left eye
H47.213 Primary optic atrophy, bilateral
H47.219 Primary optic atrophy, unspecified eye
H47.23 Glaucomatous optic atrophy
H47.231 Glaucomatous optic atrophy, right eye
H47.232 Glaucomatous optic atrophy, left eye
H47.233 Glaucomatous optic atrophy, bilateral
H47.239 Glaucomatous optic atrophy, unspecified eye
H47.29 Other optic atrophy
H47.291 Other optic atrophy, right eye
H47.292 Other optic atrophy, left eye
H47.293 Other optic atrophy, bilateral
H47.299 Other optic atrophy, unspecified eye
H47.3 Other disorders of optic disc
H47.31 Coloboma of optic disc
H47.311 Coloboma of optic disc, right eye
H47.312 Coloboma of optic disc, left eye
H47.313 Coloboma of optic disc, bilateral
H47.319 Coloboma of optic disc, unspecified eye
H47.32 Drusen of optic disc
H47.321 Drusen of optic disc, right eye
H47.322 Drusen of optic disc, left eye
H47.323 Drusen of optic disc, bilateral
H47.329 Drusen of optic disc, unspecified eye
H47.33 Pseudopapilledema of optic disc
H47.331 Pseudopapilledema of optic disc, right eye
H47.332 Pseudopapilledema of optic disc, left eye
H47.333 Pseudopapilledema of optic disc, bilateral
H47.339 Pseudopapilledema of optic disc, unspecified eye
H47.39 Other disorders of optic disc
H47.391 Other disorders of optic disc, right eye
H47.392 Other disorders of optic disc, left eye
H47.393 Other disorders of optic disc, bilateral
H47.399 Other disorders of optic disc, unspecified eye
H47.4 Disorders of optic chiasm
H47.41 Disorders of optic chiasm in (due to) inflammatory disorders
H47.42 Disorders of optic chiasm in (due to) neoplasm
H47.43 Disorders of optic chiasm in (due to) vascular disorders
H47.49 Disorders of optic chiasm in (due to) other disorders
H47.5 Disorders of other visual pathways
H47.51 Disorders of visual pathways in (due to) inflammatory disorders
H47.511 Disorders of visual pathways in (due to) inflammatory disorders, right side
H47.512 Disorders of visual pathways in (due to) inflammatory disorders, left side
H47.519 Disorders of visual pathways in (due to) inflammatory disorders, unspecified side
H47.52 Disorders of visual pathways in (due to) neoplasm
H47.521 Disorders of visual pathways in (due to) neoplasm, right side
H47.522 Disorders of visual pathways in (due to) neoplasm, left side
H47.529 Disorders of visual pathways in (due to) neoplasm, unspecified side
H47.53 Disorders of visual pathways in (due to) vascular disorders
H47.531 Disorders of visual pathways in (due to) vascular disorders, right side
H47.532 Disorders of visual pathways in (due to) vascular disorders, left side
H47.539 Disorders of visual pathways in (due to) vascular disorders, unspecified side
H47.6 Disorders of visual cortex
H47.61 Cortical blindness
H47.611 Cortical blindness, right side of brain
H47.612 Cortical blindness, left side of brain
H47.619 Cortical blindness, unspecified side of brain
H47.62 Disorders of visual cortex in (due to) inflammatory disorders
H47.621 Disorders of visual cortex in (due to) inflammatory disorders, right side of brain
H47.622 Disorders of visual cortex in (due to) inflammatory disorders, left side of brain
H47.629 Disorders of visual cortex in (due to) inflammatory disorders, unspecified side of brain
H47.63 Disorders of visual cortex in (due to) neoplasm
H47.631 Disorders of visual cortex in (due to) neoplasm, right side of brain
H47.632 Disorders of visual cortex in (due to) neoplasm, left side of brain
H47.639 Disorders of visual cortex in (due to) neoplasm, unspecified side of brain
H47.64 Disorders of visual cortex in (due to) vascular disorders
H47.641 Disorders of visual cortex in (due to) vascular disorders, right side of brain
H47.642 Disorders of visual cortex in (due to) vascular disorders, left side of brain
H47.649 Disorders of visual cortex in (due to) vascular disorders, unspecified side of brain
H47.9 Unspecified disorder of visual pathways


This page was last updated on: 10/1/2023