M04.8 OTHER AUTOINFLAMMATORY SYNDROMES

Code Information

  • Diagnosis Code: M04.8
  • Short Description: Other autoinflammatory syndromes
  • Long Description: Other autoinflammatory syndromes
  • Code Version: 2025 ICD-10-CM

The code M04.8 is VALID for claim submission

Code Classification

Synonyms

  • Acute blistering eruption of skin
  • Acute pustular skin eruption
  • Autoinflammation-PLCG2-associated antibody deficiency-immune dysregulation
  • Autoinflammatory syndrome with pyogenic bacterial infection and amylopectinosis
  • Blau syndrome
  • Bullous eruption
  • Complex multigenic autoinflammatory syndrome
  • Congenital dyserythropoietic anemia
  • Deficiency of interleukin 36 receptor antagonist
  • Generalized pustular psoriasis
  • Granulomatous inflammatory arthritis, dermatitis and uveitis, familial
  • Haploinsufficiency of A20
  • Hereditary pediatric Behçet-like disease
  • Majeed syndrome
  • Mendelian susceptibility to mycobacterial disease due to complete interleukin 12 subunit beta deficiency
  • Monogenic autoinflammatory syndrome
  • OTULIN-related autoinflammatory syndrome
  • Sporadic Blau syndrome
  • Type I interferonopathy
  • USP18 deficiency
  • Vesicular eruption
  • VEXAS syndrome
  • Yao syndrome

Diagnostic Related Group(s)

The code M04.8 is grouped in the following Diagnostic Related Group(s) MS-DRG V42.0

  1. Connective Tissue Disorders With Mcc (545)
  2. Connective Tissue Disorders With Cc (546)
  3. Connective Tissue Disorders Without Cc/mcc (547)

References to Index of Diseases and Injuries

The code M04.8 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Blau syndrome
    • Deficiency of interleukin 1 receptor antagonist [DIRA]
    • Majeed syndrome
    • Periodic fever, aphthous stomatitis, pharyngitis, and adenopathy syndrome [PFAPA]
    • Pyogenic arthritis, pyoderma gangrenosum, and acne syndrome [PAPA]

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
M04.8 Right Arrow 710.8 Diff connect tis dis NEC
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
M04 Autoinflammatory syndromes
M04.1 Periodic fever syndromes
M04.2 Cryopyrin-associated periodic syndromes
M04.9 Autoinflammatory syndrome, unspecified
This page was last updated on: 10/1/2024
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