Q00.0 ANENCEPHALY

Code Information

  • Diagnosis Code: Q00.0
  • Short Description: Anencephaly
  • Long Description: Anencephaly
  • Code Version: 2025 ICD-10-CM

The code Q00.0 is VALID for claim submission

Code Classification

Synonyms

  • Acardia
  • Acephalobrachius
  • Acephalocheiria
  • Acephaly
  • Acrania
  • Amyelencephalus
  • Anencephalus
  • Anencephaly without rachischisis
  • Congenital absence of left hand
  • Congenital absence of right hand
  • Congenital brain aplasia
  • Hemianencephaly
  • Hemicephaly
  • Holoacardius acephalus
  • Holoanencephaly
  • Incomplete anencephaly

References to Index of Diseases and Injuries

The code Q00.0 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Acephaly
    • Acrania
    • Amyelencephaly
    • Hemianencephaly
    • Hemicephaly

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q00.0 Right Arrow 740.0 Anencephalus
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q00 Anencephaly and similar malformations
Q00.1 Craniorachischisis
Q00.2 Iniencephaly
This page was last updated on: 10/1/2025
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