Q89.81 KABUKI SYNDROME

Code Information

  • Diagnosis Code: Q89.81
  • Short Description: Kabuki syndrome
  • Long Description: Kabuki syndrome
  • Code Version: 2025 ICD-10-CM

The code Q89.81 is VALID for claim submission

Code Classification

Synonyms

  • Kabuki make-up syndrome

Diagnostic Related Group(s)

The code Q89.81 is grouped in the following Diagnostic Related Group(s) MS-DRG V43.0

  1. Other Musculoskeletal System And Connective Tissue Diagnoses With Mcc (564)
  2. Other Musculoskeletal System And Connective Tissue Diagnoses With Cc (565)
  3. Other Musculoskeletal System And Connective Tissue Diagnoses Without Cc/mcc (566)

References to Index of Diseases and Injuries

The code Q89.81 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Kabuki syndrome, type 1, due to KMT2D mutation
    • Kabuki syndrome, type 2, due to KDM6A mutation
    • Niikawa-Kuroki syndrome

Similar Codes

ICD-10 Code ICD-10 Description
Q89 Other congenital malformations, not elsewhere classified
Q89.0 Congenital absence and malformations of spleen
Q89.01 Asplenia (congenital)
Q89.09 Congenital malformations of spleen
Q89.1 Congenital malformations of adrenal gland
Q89.2 Congenital malformations of other endocrine glands
Q89.3 Situs inversus
Q89.4 Conjoined twins
Q89.7 Multiple congenital malformations, not elsewhere classified
Q89.8 Other specified congenital malformations
Q89.89 Other specified congenital malformations
Q89.9 Congenital malformation, unspecified
This page was last updated on: 10/1/2025
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