333.0 DEGEN BASAL GANGLIA NEC

Code Information

  • Diagnosis Code: 333.0
  • Short Description: Degen basal ganglia NEC
  • Long Description: Other degenerative diseases of the basal ganglia
  • Code Version: 2015 ICD-9-CM

Code Classification

  • Diseases of the nervous system (320–359)
    • Hereditary and degenerative diseases of the central nervous system (330-337)
      • 333 Other extrapyramidal disease and abnormal movement disorders
        • 333.0 Degen basal ganglia NEC

Synonyms

  • Aicardi Goutieres syndrome
  • Autosomal dominant late onset basal ganglia degeneration
  • Basal ganglia degeneration with calcification
  • Choreoacanthocytosis
  • Disorder of basal ganglia
  • Fahr's syndrome
  • Juvenile paralysis agitans of Hunt
  • Multiple system atrophy
  • Multiple system atrophy, Parkinson variant
  • Neuroferritinopathy
  • Olivopontocerebellar atrophy with blindness
  • Olivopontocerebellar atrophy with slow eye movement
  • Olivopontocerebellar degeneration
  • Pallidal degeneration
  • Pallidoluysian degeneration
  • Pallidonigral degeneration
  • Pallidonigrospinal degeneration
  • Pallidopontonigral degeneration
  • Parkinsonian syndrome associated with idiopathic orthostatic hypotension
  • Parkinsonism with orthostatic hypotension
  • Pigmentary pallidal degeneration
  • Progressive supranuclear ophthalmoplegia
  • Shy-Drager syndrome
  • Sporadic olivopontocerebellar atrophy
  • Striatonigral degeneration

References to Index of Diseases and Injuries

The code 333.0 has the following ICD-9-CM references to the Index of Diseases and Injuries

  • Atrophy, atrophic
    • D�j�rine-Thomas 333.0
    • olivopontocerebellar 333.0
  • Degeneration, degenerative
    • basal nuclei or ganglia NEC 333.0
    • olivopontocerebellar (familial) (hereditary) 333.0
    • pallidal, pigmentary (progressive) 333.0
    • pigmentary (diffuse) (general)
      • pallidal (progressive) 333.0
    • strionigral 333.0
  • D�j�rine-Thomas atrophy or syndrome 333.0
  • Dementia 294.20
    • due to or associated with condition(s) classified elsewhere
      • Pelizaeus-Merzbacher disease
        • with behavioral disturbance 333.0 [294.11]
        • without behavioral disturbance 333.0 [294.10]
  • Disease, diseased - see also Syndrome
    • basal ganglia 333.90
      • degenerative NEC 333.0
    • Hallervorden-Spatz 333.0
  • Hallervorden-Spatz disease or syndrome 333.0
  • Hypotension (arterial) (constitutional) 458.9
    • orthostatic (chronic) 458.0
      • dysautonomic-dyskinetic syndrome 333.0
  • Insufficiency, insufficient
    • idiopathic autonomic 333.0
  • Ophthalmoplegia (see also Strabismus) 378.9
    • supranuclear, progressive 333.0
  • Palsy (see also Paralysis) 344.9
    • progressive supranuclear 333.0
    • supranuclear NEC 356.8
      • progressive 333.0
  • Parkinsonism (arteriosclerotic) (idiopathic) (primary) 332.0
    • associated with orthostatic hypotension (idiopathic) (symptomatic) 333.0
  • Shy-Drager syndrome (orthostatic hypotension with multisystem degeneration) 333.0
  • Steele-Richardson (-Olszewski) Syndrome 333.0
  • Syndrome - see also Disease
    • D�j�rine-Thomas 333.0
    • Hallervorden-Spatz 333.0
    • orthostatic hypotensive-dysautonomic-dyskinetic 333.0
    • progressive pallidal degeneration 333.0
    • Shy-Drager (orthostatic hypotension with multisystem degeneration) 333.0

Crosswalk Information

The code 333.0 converts into the following ICD-10 code(s):

ICD-9 Code ICD-10 Code ICD-10 Description
333.0 Right Arrow G23.0 Hallervorden-Spatz disease
G23.1 Progressive supranuclear ophthalmoplegia
G23.2 Striatonigral degeneration
G23.8 Other specified degenerative diseases of basal ganglia
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
333.1 Essential and other specified forms of tremor
333.2 Myoclonus
333.3 Tics of organic origin
333.4 Huntington's chorea
333.5 Other choreas
333.6 Genetic torsion dystonia
333.71 Athetoid cerebral palsy
333.72 Acute dystonia due to drugs
333.79 Other acquired torsion dystonia
333.81 Blepharospasm
333.82 Orofacial dyskinesia
333.83 Spasmodic torticollis
333.84 Organic writers' cramp
333.85 Subacute dyskinesia due to drugs
333.89 Other fragments of torsion dystonia
333.90 Unspecified extrapyramidal disease and abnormal movement disorder
333.91 Stiff-man syndrome
333.92 Neuroleptic malignant syndrome
333.93 Benign shuddering attacks
333.94 Restless legs syndrome (RLS)
333.99 Other extrapyramidal diseases and abnormal movement disorders
This page was last updated on: 10/1/2014
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