742.3 CONGENITAL HYDROCEPHALUS

Code Information

Diagnosis Code: 742.3
Short Description: Congenital hydrocephalus
Long Description: Congenital hydrocephalus
Code Version: 2015 ICD-9-CM

Code Classification

Congenital anomalies (740–759)
- Congenital anomalies (740-759)
  - 742 Other congenital anomalies of nervous system
    - 742.3 Congenital hydrocephalus

References to Index of Diseases and Injuries

The code 742.3 has the following ICD-9-CM references to the Index of Diseases and Injuries

Absence (organ or part) (complete or partial)
- skull bone 756.0
  - with
    - hydrocephalus 742.3
      - with spina bifida (see also Spina bifida) 741.0

Agenesis - see also Absence, by site, congenital
- skull (bone) 756.0
  - with
    - hydrocephalus 742.3
      - with spina bifida (see also Spina bifida) 741.0

Anomaly, anomalous (congenital) (unspecified type) 759.9
- aqueduct of Sylvius 742.3
  - with spina bifida (see also Spina bifida) 741.0
- bone NEC 756.9
  - skull 756.0
    - with
      - hydrocephalus 742.3
        with spina bifida (see also Spina bifida) 741.0
- skull (bone) 756.0
  - with
    - hydrocephalus 742.3
      - with spina bifida (see also Spina bifida) 741.0
- specified type NEC
  - bone(s) 756.9
    - skull 756.0
      - with
        hydrocephalus 742.3
  - skull (bone(s)) 756.0
    - with
      - hydrocephalus 742.3
        with spina bifida (see also Spina bifida) 741.0

Atresia, atretic (congenital) 759.89
- aqueduct of Sylvius 742.3
  - with spina bifida (see also Spina bifida) 741.0
- foramen of
  - Luschka 742.3
    - with spina bifida (see also Spina bifida) 741.0
  - Magendie 742.3
    - with spina bifida (see also Spina bifida) 741.0

Block
- foramen Magendie (acquired) 331.3
  - congenital 742.3
    - with spina bifida (see also Spina bifida) 741.0

Cyst (mucus) (retention) (serous) (simple)
- Dandy-Walker 742.3
  - with spina bifida (see also Spina bifida) 741.0

Dandy-Walker deformity or syndrome (atresia, foramen of Magendie) 742.3
- with spina bifida (see also Spina bifida) 741.0

Deformity 738.9
- Dandy-Walker 742.3
  - with spina bifida (see also Spina bifida) 741.0
- skull (acquired) 738.19
  - congenital 756.0
    - with
      - hydrocephalus 742.3
        with spina bifida (see also Spina bifida) 741.0

Degeneration, degenerative
- brain (cortical) (progressive) 331.9
  - in
    - congenital hydrocephalus 742.3 [331.7]
      - with spina bifida (see also Spina bifida) 741.0 [331.7]

Distortion (congenital)
- skull bone(s) 756.0
  - with
    - hydrocephalus 742.3
      - with spina bifida (see also Spina bifida) 741.0

Forking, aqueduct of Sylvius 742.3
- with spina bifida (see also Spina bifida) 741.0

Hydrancephaly 742.3
- with spina bifida (see also Spina bifida) 741.0

Hydranencephaly 742.3
- with spina bifida (see also Spina bifida) 741.0

Hydrocephalus (acquired) (external) (internal) (malignant) (noncommunicating) (obstructive) (recurrent) 331.4
- aqueduct of Sylvius stricture 742.3
  - with spina bifida (see also Spina bifida) 741.0
- chronic 742.3
  - with spina bifida (see also Spina bifida) 741.0
- congenital (external) (internal) 742.3
  - with spina bifida (see also Spina bifida) 741.0
- due to
  - stricture of aqueduct of Sylvius 742.3
    - with spina bifida (see also Spina bifida) 741.0
- foramen Magendie block (acquired) 331.3
  - congenital 742.3
    - with spina bifida (see also Spina bifida) 741.0
- newborn 742.3
  - with spina bifida (see also Spina bifida) 741.0

Hypoplasia, hypoplasis 759.89
- skull (bone) 756.0
  - with
    - hydrocephalus 742.3
      - with spina bifida (see also Spina bifida) 741.0

Imperfect
- closure (congenital)
  - skull 756.0
    - with
      - hydrocephalus 742.3
        with spina bifida (see also Spina bifida) 741.0

Obstruction, obstructed, obstructive
- aqueduct of Sylvius 331.4
  - congenital 742.3
    - with spina bifida (see also Spina bifida) 741.0
- foramen of Monro (congenital) 742.3
  - with spina bifida (see also Spina bifida) 741.0

Occlusion
- aqueduct of Sylvius 331.4
  - congenital 742.3
    - with spina bifida (see also Spina bifida) 741.0

Paratyphoid (fever) - see Fever, paratyphoid

Septum, septate (congenital) - see also Anomaly, specified type NEC
- aqueduct of Sylvius 742.3
  - with spina bifida (see also Spina bifida) 741.0

Stenosis (cicatricial) - see also Stricture
- aqueduct of Sylvius (congenital) 742.3
  - with spina bifida (see also Spina bifida) 741.0
  - acquired 331.4

Stricture (see also Stenosis) 799.89
- aqueduct of Sylvius (congenital) 742.3
  - with spina bifida (see also Spina bifida) 741.0
  - acquired 331.4

Syndrome - see also Disease
- Dandy-Walker (atresia, foramen of Magendie) 742.3
  - with spina bifida (see also Spina bifida) 741.0

Crosswalk Information

The code 742.3 converts into the following ICD-10 code(s):

ICD-9 Code	ICD-10 Code	ICD-10 Description
742.3	Q03.0	Malformations of aqueduct of Sylvius
	Q03.1	Atresia of foramina of Magendie and Luschka
	Q03.8	Other congenital hydrocephalus

This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code	ICD-9 Description
742.0	Encephalocele
742.1	Microcephalus
742.2	Congenital reduction deformities of brain
742.4	Other specified congenital anomalies of brain
742.51	Diastematomyelia
742.53	Hydromyelia
742.59	Other specified congenital anomalies of spinal cord
742.8	Other specified congenital anomalies of nervous system
742.9	Unspecified congenital anomaly of brain, spinal cord, and nervous system

This page was last updated on: 10/1/2014

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