Diagnosis Code


Code Information

Diagnosis Code: A81.00

Short Description: Creutzfeldt-Jakob disease, unspecified

Long Description: Creutzfeldt-Jakob disease, unspecified

The code A81.00 is VALID for claim submission

Code Classification:

  • Certain infectious and parasitic diseases (A00–B99)
    • Viral and prion infections of the central nervous system (A80-A89)
      • Atypical virus infections of central nervous system (A81)
        • A81.00 Creutzfeldt-Jakob disease, unspecified

Code Version: 2020 ICD-10-CM


  • Cerebral degeneration due to Creutzfeldt-Jakob disease
  • Creutzfeldt-Jakob disease
  • Dementia due to Creutzfeldt Jakob disease
  • Dementia due to infectious disease

References to Index of Diseases and Injuries

The code A81.00 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Jakob-Creutzfeldt disease, unspecified

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
A81.00 Right Arrow 046.19 Creutzfldt-Jakob NEC/NOS

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
A81 Atypical virus infections of central nervous system
A81.0 Creutzfeldt-Jakob disease
A81.01 Variant Creutzfeldt-Jakob disease
A81.09 Other Creutzfeldt-Jakob disease
A81.1 Subacute sclerosing panencephalitis
A81.2 Progressive multifocal leukoencephalopathy
A81.8 Other atypical virus infections of central nervous system
A81.81 Kuru
A81.82 Gerstmann-Straussler-Scheinker syndrome
A81.83 Fatal familial insomnia
A81.89 Other atypical virus infections of central nervous system
A81.9 Atypical virus infection of central nervous system, unspecified

This page was last updated on: 10/1/2019