Diagnosis Code


Code Information

Diagnosis Code: A81.82

Short Description: Gerstmann-Straussler-Scheinker syndrome

Long Description: Gerstmann-Straussler-Scheinker syndrome

The code A81.82 is VALID for claim submission

Code Classification:

  • Certain infectious and parasitic diseases (A00–B99)
    • Viral and prion infections of the central nervous system (A80-A89)
      • Atypical virus infections of central nervous system (A81)
        • A81.82 Gerstmann-Straussler-Scheinker syndrome

Code Version: 2022 ICD-10-CM


  • Dementia due to genetic disease
  • Dementia due to Gerstmann Straussler Scheinker syndrome
  • Dementia due to prion disease
  • Gerstmann-Straussler-Scheinker syndrome

References to Index of Diseases and Injuries

The code A81.82 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • GSS syndrome

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
A81.82 Right Arrow 046.71 Gerstmn-Straus-Schnk syn

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
A81 Atypical virus infections of central nervous system
A81.0 Creutzfeldt-Jakob disease
A81.00 Creutzfeldt-Jakob disease, unspecified
A81.01 Variant Creutzfeldt-Jakob disease
A81.09 Other Creutzfeldt-Jakob disease
A81.1 Subacute sclerosing panencephalitis
A81.2 Progressive multifocal leukoencephalopathy
A81.8 Other atypical virus infections of central nervous system
A81.81 Kuru
A81.83 Fatal familial insomnia
A81.89 Other atypical virus infections of central nervous system
A81.9 Atypical virus infection of central nervous system, unspecified

This page was last updated on: 10/1/2023