Diagnosis Code

D68.2 HEREDITARY DEFICIENCY OF OTHER CLOTTING FACTORS


Code Information

Diagnosis Code: D68.2

Short Description: Hereditary deficiency of other clotting factors

Long Description: Hereditary deficiency of other clotting factors

The code D68.2 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
      • Other coagulation defects (D68)
        • D68.2 Hereditary deficiency of other clotting factors

Code Version: 2022 ICD-10-CM


Synonyms

  • Acquired coagulation factor inhibitor disorder
  • Alpha chain defect dysfibrinogenemia
  • Autosomal dominant deficiency of plasminogen
  • Beta chain defect dysfibrinogenemia
  • Combined deficiency of factor V and factor VIII
  • Congenital afibrinogenemia
  • Congenital fibrinogen abnormality
  • Congenital plasminogen activator inhibitor deficiency type 1
  • Contact factor deficiency
  • Drug-induced coagulation inhibitor disorder
  • Dysfibrinogenemia
  • Dysplasminogenemia
  • Factor I deficiency
  • Factor I deficiency
  • Factor I deficiency disease
  • Factor II deficiency
  • Factor V deficiency
  • Factor V deficiency
  • Factor VII deficiency
  • Factor X deficiency
  • Factor XII deficiency disease
  • Factor XIII deficiency disease
  • Factor XIII inhibitor disorder
  • Fibrinogen abnormality
  • Fibrinogen deficiency
  • Fibrinogen in blood above reference range
  • Fibrinolytic bleeding syndrome
  • Gamma chain defect dysfibrinogenemia
  • Hemorrhagic disease of the newborn due to factor II deficiency
  • Heparin cofactor II deficiency
  • Hereditary combined coagulation factor deficiency
  • Hereditary combined coagulation factor deficiency
  • Hereditary combined deficiency of vitamin K-dependent clotting factors
  • Hereditary congenital prekallikrein deficiency
  • Hereditary dysfibrinogenemia
  • Hereditary dysplasminogenemia
  • Hereditary factor I deficiency disease
  • Hereditary factor II deficiency disease
  • Hereditary factor V deficiency disease
  • Hereditary factor VII deficiency disease
  • Hereditary factor X deficiency disease
  • Hereditary factor XII deficiency disease
  • Hereditary factor XIII A subunit and B subunit deficiency
  • Hereditary factor XIII A subunit deficiency
  • Hereditary factor XIII B subunit deficiency
  • Hereditary factor XIII deficiency disease
  • Hereditary hypoplasminogenemia
  • Hereditary thrombophilic dysfibrinogenemia
  • High molecular weight kininogen deficiency
  • Hyperfibrinogenemia
  • Hypodysfibrinogenemia
  • Hypoplasminogenemia
  • Immunodeficiency with factor I anomaly
  • Neonatal coagulation disorder
  • Passovoy factor deficiency
  • Platelet factor V deficiency
  • Platelet procoagulant activity deficiency
  • Prekallikrein deficiency
  • Prothrombin complex deficiency

References to Index of Diseases and Injuries

The code D68.2 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • AC globulin deficiency
    • Congenital afibrinogenemia
    • Deficiency of factor I [fibrinogen]
    • Deficiency of factor II [prothrombin]
    • Deficiency of factor V [labile]
    • Deficiency of factor VII [stable]
    • Deficiency of factor X [Stuart-Prower]
    • Deficiency of factor XII [Hageman]
    • Deficiency of factor XIII [fibrin stabilizing]
    • Dysfibrinogenemia (congenital)
    • Hypoproconvertinemia
    • Owren's disease
    • Proaccelerin deficiency

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D68.2 Right Arrow 286.3 Cong def clot factor NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D68 Other coagulation defects
D68.0 Von Willebrand disease
D68.00 Von Willebrand disease, unspecified
D68.01 Von Willebrand disease, type 1
D68.02 Von Willebrand disease, type 2
D68.020 Von Willebrand disease, type 2A
D68.021 Von Willebrand disease, type 2B
D68.022 Von Willebrand disease, type 2M
D68.023 Von Willebrand disease, type 2N
D68.029 Von Willebrand disease, type 2, unspecified
D68.03 Von Willebrand disease, type 3
D68.04 Acquired von Willebrand disease
D68.09 Other von Willebrand disease
D68.1 Hereditary factor XI deficiency
D68.3 Hemorrhagic disorder due to circulating anticoagulants
D68.31 Hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.311 Acquired hemophilia
D68.312 Antiphospholipid antibody with hemorrhagic disorder
D68.318 Other hemorrhagic disorder due to intrinsic circulating anticoagulants, antibodies, or inhibitors
D68.32 Hemorrhagic disorder due to extrinsic circulating anticoagulants
D68.4 Acquired coagulation factor deficiency
D68.5 Primary thrombophilia
D68.51 Activated protein C resistance
D68.52 Prothrombin gene mutation
D68.59 Other primary thrombophilia
D68.6 Other thrombophilia
D68.61 Antiphospholipid syndrome
D68.62 Lupus anticoagulant syndrome
D68.69 Other thrombophilia
D68.8 Other specified coagulation defects
D68.9 Coagulation defect, unspecified


This page was last updated on: 10/1/2023