Diagnosis Code

D74.0 CONGENITAL METHEMOGLOBINEMIA


Code Information

Diagnosis Code: D74.0

Short Description: Congenital methemoglobinemia

Long Description: Congenital methemoglobinemia

The code D74.0 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Other disorders of blood and blood-forming organs (D70-D77)
      • Methemoglobinemia (D74)
        • D74.0 Congenital methemoglobinemia

Code Version: 2022 ICD-10-CM


Synonyms

  • Autosomal recessive congenital methemoglobinemia
  • Autosomal recessive congenital methemoglobinemia type I
  • Autosomal recessive congenital methemoglobinemia type II
  • Congenital methemoglobinaema with defective methemoglobin-reducing system
  • Congenital methemoglobinemia
  • Congenital methemoglobinemia with abnormal methemoglobins
  • Familial methemoglobinemia
  • Hemoglobin M disease

Diagnostic Related Group(s)

The code D74.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Red Blood Cell Disorders With Mcc (811)
  • Red Blood Cell Disorders Without Mcc (812)

References to Index of Diseases and Injuries

The code D74.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Congenital NADH-methemoglobin reductase deficiency
    • Hemoglobin-M [Hb-M] disease
    • Methemoglobinemia, hereditary

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D74.0 Right Arrow 289.7 Methemoglobinemia

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D74 Methemoglobinemia
D74.8 Other methemoglobinemias
D74.9 Methemoglobinemia, unspecified


This page was last updated on: 10/1/2023