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Diagnosis Code

D76.3 OTHER HISTIOCYTOSIS SYNDROMES


Code Information

Diagnosis Code: D76.3

Short Description: Other histiocytosis syndromes

Long Description: Other histiocytosis syndromes

The code D76.3 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Other disorders of blood and blood-forming organs (D70-D77)
      • Oth dis with lymphoreticular and reticulohistiocytic tissue (D76)
        • D76.3 Other histiocytosis syndromes

Code Version: 2022 ICD-10-CM


Synonyms

  • Benign cephalic histiocytosis
  • Chronic histiocytosis
  • Cutaneous reticulohistiocytosis
  • Dermal dendritic cell histiocytosis
  • Erdheim-Chester disease
  • Hemolytic erythrophagocytic syndrome
  • Hereditary progressive mucinous histiocytosis
  • Histiocytic syndrome
  • Histiocytosis-lymphadenopathy plus syndrome
  • Juvenile xanthogranuloma
  • Juvenile xanthogranuloma of iris
  • Juvenile xanthogranuloma of skin
  • Malakoplakia
  • Malakoplakia
  • Mucinous histiocytosis of the colon
  • Multiple eruptive juvenile xanthogranuloma
  • Necrobiotic xanthogranuloma
  • Necrobiotic xanthogranuloma with paraproteinemia
  • Non-Langerhans cell histiocytic dermatosis
  • Panniculitis secondary to histiocytic disorder
  • Periodontitis due to histiocytosis syndrome
  • Progressive nodular histiocytosis
  • Retroperitoneal xanthogranuloma
  • Sea-blue histiocyte syndrome
  • Sinus histiocytosis with massive lymphadenopathy
  • Solitary eruptive xanthogranuloma
  • Solitary reticulohistiocytoma
  • Subcutaneous xanthogranulomatosis
  • Undetermined cell histiocytosis
  • Xanthogranuloma
  • Xanthogranuloma
  • Xanthogranuloma
  • Xanthogranuloma of choroid plexus

Diagnostic Related Group(s)

The code D76.3 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Reticuloendothelial And Immunity Disorders With Mcc (814)
  • Reticuloendothelial And Immunity Disorders With Cc (815)
  • Reticuloendothelial And Immunity Disorders Without Cc/mcc (816)

References to Index of Diseases and Injuries

The code D76.3 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Reticulohistiocytoma (giant-cell)
    • Sinus histiocytosis with massive lymphadenopathy
    • Xanthogranuloma

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D76.3 Right Arrow 288.4 Hemophagocytic syndromes

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D76 Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue
D76.1 Hemophagocytic lymphohistiocytosis
D76.2 Hemophagocytic syndrome, infection-associated

This page was last updated on: 10/1/2023

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