Diagnosis Code

D80.2 SELECTIVE DEFICIENCY OF IMMUNOGLOBULIN A [IGA]


Code Information

Diagnosis Code: D80.2

Short Description: Selective deficiency of immunoglobulin A [IgA]

Long Description: Selective deficiency of immunoglobulin A [IgA]

The code D80.2 is VALID for claim submission

Code Classification:

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
    • Certain disorders involving the immune mechanism (D80-D89)
      • Immunodeficiency with predominantly antibody defects (D80)
        • D80.2 Selective deficiency of immunoglobulin A [IgA]

Code Version: 2022 ICD-10-CM


Synonyms

  • Alpha globulin level outside reference range
  • Chromosome 22 abnormalities with hypogammaglobulinemia
  • Deficiency of immunoglobulin A with immunoglobulin G subclass deficiency
  • Humoral immune defect
  • Hypoalphaglobulinemia
  • Immune defect
  • Immunoglobulin A deficiency
  • Immunoglobulin A deficiency
  • Immunoglobulin A1 deficiency
  • Immunoglobulin A2 deficiency
  • Immunoglobulin G subclass deficiency
  • Immunoglobulin heavy chain deficiency
  • Immunoglobulin heavy chain deficiency
  • Monosomy 22 and absence of immunoglobulin A
  • Selective immunoglobulin A deficiency
  • Selective immunoglobulin M and immunoglobulin A deficiency

Diagnostic Related Group(s)

The code D80.2 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Reticuloendothelial And Immunity Disorders With Mcc (814)
  • Reticuloendothelial And Immunity Disorders With Cc (815)
  • Reticuloendothelial And Immunity Disorders Without Cc/mcc (816)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
D80.2 Right Arrow 279.01 Selective iga immunodef

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
D80 Immunodeficiency with predominantly antibody defects
D80.0 Hereditary hypogammaglobulinemia
D80.1 Nonfamilial hypogammaglobulinemia
D80.3 Selective deficiency of immunoglobulin G [IgG] subclasses
D80.4 Selective deficiency of immunoglobulin M [IgM]
D80.5 Immunodeficiency with increased immunoglobulin M [IgM]
D80.6 Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
D80.7 Transient hypogammaglobulinemia of infancy
D80.8 Other immunodeficiencies with predominantly antibody defects
D80.9 Immunodeficiency with predominantly antibody defects, unspecified


This page was last updated on: 10/1/2023