Diagnosis Code

E31.0 AUTOIMMUNE POLYGLANDULAR FAILURE


Code Information

Diagnosis Code: E31.0

Short Description: Autoimmune polyglandular failure

Long Description: Autoimmune polyglandular failure

The code E31.0 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Disorders of other endocrine glands (E20-E35)
      • Polyglandular dysfunction (E31)
        • E31.0 Autoimmune polyglandular failure

Code Version: 2022 ICD-10-CM


Synonyms

  • A. Schmidt's syndrome
  • Addison's disease
  • Autoimmune enteropathy
  • Autoimmune enteropathy and endocrinopathy with susceptibility to chronic infection syndrome
  • Autoimmune hypoparathyroidism
  • Autoimmune polyendocrine syndrome type 3
  • Autoimmune polyendocrine syndrome type 4
  • Autoimmune polyendocrinopathy
  • Chronic mucocutaneous candidiasis
  • Multiple cranial nerve palsy
  • Polyglandular autoimmune syndrome, type 1
  • Polyglandular autoimmune syndrome, type 2

Diagnostic Related Group(s)

The code E31.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Endocrine Disorders With Mcc (643)
  • Endocrine Disorders With Cc (644)
  • Endocrine Disorders Without Cc/mcc (645)

References to Index of Diseases and Injuries

The code E31.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Schmidt's syndrome

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E31.0 Right Arrow 258.1 Comb endocr dysfunct NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E31 Polyglandular dysfunction
E31.1 Polyglandular hyperfunction
E31.2 Multiple endocrine neoplasia [MEN] syndromes
E31.20 Multiple endocrine neoplasia [MEN] syndrome, unspecified
E31.21 Multiple endocrine neoplasia [MEN] type I
E31.22 Multiple endocrine neoplasia [MEN] type IIA
E31.23 Multiple endocrine neoplasia [MEN] type IIB
E31.8 Other polyglandular dysfunction
E31.9 Polyglandular dysfunction, unspecified


This page was last updated on: 10/1/2023