Diagnosis Code

E74.21 GALACTOSEMIA


Code Information

Diagnosis Code: E74.21

Short Description: Galactosemia

Long Description: Galactosemia

The code E74.21 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Other disorders of carbohydrate metabolism (E74)
        • E74.21 Galactosemia

Code Version: 2022 ICD-10-CM


Synonyms

  • Classical galactosemia, heterozygous type
  • Classical galactosemia, homozygous Duarte-type
  • Classical galactosemia, homozygous Negro-type
  • Deficiency of galactose mutarotase
  • Deficiency of UDPglucose-hexose-1-phosphate uridylyltransferase
  • Deficiency of UTP-hexose-1-phosphate uridylyltransferase
  • Deficiency of UTP-hexose-1-phosphate uridylyltransferase
  • Deficiency of UTP-hexose-1-phosphate uridylyltransferase
  • Disorder of galactose metabolism
  • Disorder of galactose metabolism
  • Disorder of galactose metabolism
  • Disorder of galactose metabolism
  • Disorder of galactose metabolism
  • Disorder of galactose metabolism
  • Erythrocyte uridine diphosphate galactose-4-epimerase deficiency
  • Galactose epimerase deficiency
  • Galactosemia
  • Generalized uridine diphosphate galactose-4-epimerase deficiency
  • Perinatal jaundice due to galactosemia

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E74.21 Right Arrow 271.1 Galactosemia

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E74 Other disorders of carbohydrate metabolism
E74.0 Glycogen storage disease
E74.00 Glycogen storage disease, unspecified
E74.01 von Gierke disease
E74.02 Pompe disease
E74.03 Cori disease
E74.04 McArdle disease
E74.05 Lysosome-associated membrane protein 2 [LAMP2] deficiency
E74.09 Other glycogen storage disease
E74.1 Disorders of fructose metabolism
E74.10 Disorder of fructose metabolism, unspecified
E74.11 Essential fructosuria
E74.12 Hereditary fructose intolerance
E74.19 Other disorders of fructose metabolism
E74.2 Disorders of galactose metabolism
E74.20 Disorders of galactose metabolism, unspecified
E74.29 Other disorders of galactose metabolism
E74.3 Other disorders of intestinal carbohydrate absorption
E74.31 Sucrase-isomaltase deficiency
E74.39 Other disorders of intestinal carbohydrate absorption
E74.4 Disorders of pyruvate metabolism and gluconeogenesis
E74.8 Other specified disorders of carbohydrate metabolism
E74.81 Disorders of glucose transport, not elsewhere classified
E74.810 Glucose transporter protein type 1 deficiency
E74.818 Other disorders of glucose transport
E74.819 Disorders of glucose transport, unspecified
E74.89 Other specified disorders of carbohydrate metabolism
E74.9 Disorder of carbohydrate metabolism, unspecified


This page was last updated on: 10/1/2023