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Taxonomy Codes
E78.79 OTHER DISORDERS OF BILE ACID AND CHOLESTEROL METABOLISM
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ICD-10 List
E00–E89
E70-E88
E78
E78.79
Code Information
Diagnosis Code:
E78.79
Short Description:
Other disorders of bile acid and cholesterol metabolism
Long Description:
Other disorders of bile acid and cholesterol metabolism
Code Version:
2025 ICD-10-CM
The code E78.79 is VALID for claim submission
Code Classification
Endocrine, nutritional and metabolic diseases (E00–E89)
Metabolic disorders (E70-E88)
Disorders of lipoprotein metabolism and other lipidemias (E78)
Synonyms
Bile acid CoA ligase deficiency and defective amidation
Bile acid malabsorption syndrome
Bile acid malabsorption syndrome
Bile acid malabsorption syndrome type I
Bile acid malabsorption syndrome type II
Cholesterol tophus
Deficiency of cholate-CoA ligase
Deficiency of cholesterol esterase
Deficiency of cholesterol oxidase
Delta-4-3-oxosteroid-5-beta-reductase deficiency
Desmosterolosis
Disorder of cholesterol catabolism
Disorder of cholesterol metabolism
Disorder of cholesterol metabolism
Disorder of cholesterol metabolism
Disorder of cholesterol synthesis
Disorder of cholesterol synthesis
Familial hypercholanemia
Intestinal malabsorption
Intestinal malabsorption due to bile acid synthesis defect
Lathosterolosis
Neonatal osteosclerotic dysplasia
Synthetic defect of bile acids
Synthetic defect of bile acids
Synthetic defect of bile acids
Crosswalk Information
ICD-10 Code
ICD-9 Code
ICD-9 Description
E78.79
272.8
Lipoid metabol dis NEC
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.
Similar Codes
ICD-10 Code
ICD-10 Description
E78
Disorders of lipoprotein metabolism and other lipidemias
E78.0
Pure hypercholesterolemia
E78.00
Pure hypercholesterolemia, unspecified
E78.01
Familial hypercholesterolemia
E78.1
Pure hyperglyceridemia
E78.2
Mixed hyperlipidemia
E78.3
Hyperchylomicronemia
E78.4
Other hyperlipidemia
E78.41
Elevated Lipoprotein(a)
E78.49
Other hyperlipidemia
E78.5
Hyperlipidemia, unspecified
E78.6
Lipoprotein deficiency
E78.7
Disorders of bile acid and cholesterol metabolism
E78.70
Disorder of bile acid and cholesterol metabolism, unspecified
E78.71
Barth syndrome
E78.72
Smith-Lemli-Opitz syndrome
E78.8
Other disorders of lipoprotein metabolism
E78.81
Lipoid dermatoarthritis
E78.89
Other lipoprotein metabolism disorders
E78.9
Disorder of lipoprotein metabolism, unspecified
This page was last updated on: 10/1/2024
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