E83.821 ENPP1 DEFICIENCY CAUSING GEN ARTERIAL CALCIFCN OF INFANCY

Code Information

  • Diagnosis Code: E83.821
  • Short Description: ENPP1 deficiency causing gen arterial calcifcn of infancy
  • Long Description: ENPP1 deficiency causing generalized arterial calcification of infancy
  • Code Version: 2025 ICD-10-CM

The code E83.821 is VALID for claim submission

Code Classification

Diagnostic Related Group(s)

The code E83.821 is grouped in the following Diagnostic Related Group(s) MS-DRG V42.0

  1. Peripheral Vascular Disorders With Mcc (299)
  2. Peripheral Vascular Disorders With Cc (300)
  3. Peripheral Vascular Disorders Without Cc/mcc (301)

References to Index of Diseases and Injuries

The code E83.821 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Code Also:
    • , if applicable, associated conditions such as:
    • heart failure (@I50*.-)
    • other secondary hypertension (@I15.8*)

Similar Codes

ICD-10 Code ICD-10 Description
E83 Disorders of mineral metabolism
E83.0 Disorders of copper metabolism
E83.00 Disorder of copper metabolism, unspecified
E83.01 Wilson's disease
E83.09 Other disorders of copper metabolism
E83.1 Disorders of iron metabolism
E83.10 Disorder of iron metabolism, unspecified
E83.11 Hemochromatosis
E83.110 Hereditary hemochromatosis
E83.111 Hemochromatosis due to repeated red blood cell transfusions
E83.118 Other hemochromatosis
E83.119 Hemochromatosis, unspecified
E83.19 Other disorders of iron metabolism
E83.2 Disorders of zinc metabolism
E83.3 Disorders of phosphorus metabolism and phosphatases
E83.30 Disorder of phosphorus metabolism, unspecified
E83.31 Familial hypophosphatemia
E83.32 Hereditary vitamin D-dependent rickets (type 1) (type 2)
E83.39 Other disorders of phosphorus metabolism
E83.4 Disorders of magnesium metabolism
E83.40 Disorders of magnesium metabolism, unspecified
E83.41 Hypermagnesemia
E83.42 Hypomagnesemia
E83.49 Other disorders of magnesium metabolism
E83.5 Disorders of calcium metabolism
E83.50 Unspecified disorder of calcium metabolism
E83.51 Hypocalcemia
E83.52 Hypercalcemia
E83.59 Other disorders of calcium metabolism
E83.8 Other disorders of mineral metabolism
E83.81 Hungry bone syndrome
E83.82 Disorders of pyrophosphate metabolism
E83.820 Generalized arterial calcification of infancy with unspecified genetic causality
E83.822 ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
E83.823 ABCC6 deficiency causing generalized arterial calcification of infancy
E83.824 ABCC6 deficiency causing pseudoxanthoma elasticum
E83.825 CD73 deficiency causing arterial calcification
E83.89 Other disorders of mineral metabolism
E83.9 Disorder of mineral metabolism, unspecified
This page was last updated on: 10/1/2025