Diagnosis Code

E84.0 CYSTIC FIBROSIS WITH PULMONARY MANIFESTATIONS


Code Information

Diagnosis Code: E84.0

Short Description: Cystic fibrosis with pulmonary manifestations

Long Description: Cystic fibrosis with pulmonary manifestations

The code E84.0 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Cystic fibrosis (E84)
        • E84.0 Cystic fibrosis with pulmonary manifestations

Code Version: 2022 ICD-10-CM


Synonyms

  • Cystic fibrosis of the lung

Diagnostic Related Group(s)

The code E84.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Respiratory Infections And Inflammations With Mcc (177)
  • Respiratory Infections And Inflammations With Cc (178)
  • Respiratory Infections And Inflammations Without Cc/mcc (179)

References to Index of Diseases and Injuries

The code E84.0 has the following ICD-10-CM references to the Index of Diseases and Injuries

    Crosswalk Information

    ICD-10 Code ICD-9 Code ICD-9 Description
    E84.0 Right Arrow 277.02 Cystic fibros w pul man

    This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

    Similar Codes

    ICD-10 Code ICD-10 Description
    E84 Cystic fibrosis
    E84.1 Cystic fibrosis with intestinal manifestations
    E84.11 Meconium ileus in cystic fibrosis
    E84.19 Cystic fibrosis with other intestinal manifestations
    E84.8 Cystic fibrosis with other manifestations
    E84.9 Cystic fibrosis, unspecified


    This page was last updated on: 10/1/2023