Diagnosis Code: G71.3

Short Description: Mitochondrial myopathy, not elsewhere classified

Long Description: Mitochondrial myopathy, not elsewhere classified

The code G71.3 is VALID for claim submission

Code Classification:

• Diseases of the nervous system (G00–G99)
  • Diseases of myoneural junction and muscle (G70-G73)
    • Primary disorders of muscles (G71)
      • G71.3 Mitochondrial myopathy, not elsewhere classified

Code Version: 2022 ICD-10-CM

Synonyms

• Adult-onset chronic progressive external ophthalmoplegia with mitochondrial myopathy
• Adult-onset multiple mitochondrial deoxyribonucleic acid deletion syndrome due to deoxyguanosine kinase deficiency
• Autosomal dominant mitochondrial myopathy with exercise intolerance
• Childhood myocerebrohepatopathy spectrum
• Congenital cataract, hypertrophic cardiomyopathy, mitochondrial myopathy syndrome
• Cytochrome-c oxidase deficiency
• DNA2-related mitochondrial DNA deletion syndrome
• FASTKD2-related infantile mitochondrial encephalomyopathy
• FBXL4-related encephalomyopathic mitochondrial DNA depletion syndrome
• Hereditary cerebellar atrophy
• Hypertrophic mitochondrial cardiomyopathy
• Lethal infantile mitochondrial myopathy
• Maternally inherited mitochondrial cardiomyopathy
• Maternally inherited mitochondrial cardiomyopathy and myopathy
• Maternally inherited mitochondrial deoxyribonucleic acid disease
• Maternally inherited mitochondrial deoxyribonucleic acid disease
• Maternally inherited mitochondrial deoxyribonucleic acid disease
• Maternally inherited mitochondrial myopathy
• Mitochondrial deoxyribonucleic acid depletion syndrome myopathic form
• Mitochondrial DNA depletion syndrome encephalomyopathic form
• Mitochondrial DNA depletion syndrome encephalomyopathic form
• Mitochondrial DNA depletion syndrome encephalomyopathic form
• Mitochondrial DNA depletion syndrome encephalomyopathic form
• Mitochondrial DNA depletion syndrome encephalomyopathic form with methylmalonic aciduria
• Mitochondrial DNA depletion syndrome, encephalomyopathic form with variable craniofacial anomalies
• Mitochondrial encephalomyopathy
• Mitochondrial myopathy
• Mitochondrial myopathy with reversible cytochrome C oxidase deficiency
• Mitochondrial myopathy with sideroblastic anemia syndrome
• Mitochondrial myopathy, cerebellar ataxia, pigmentary retinopathy syndrome
• Mitochondrial myopathy, lactic acidosis, deafness syndrome
• Mitochondrial neurogastrointestinal encephalomyopathy syndrome
• Myopathy and diabetes mellitus
• Progressive external ophthalmoplegia, myopathy, emaciation syndrome
• Pure mitochondrial myopathy
• RRM2B-related mitochondrial DNA depletion syndrome, encephalomyopathic form with renal tubulopathy
• Severe X-linked mitochondrial encephalomyopathy
• TK2-related mitochondrial deoxyribonucleic acid depletion syndrome myopathic form
• TMEM70 related mitochondrial encephalo-cardio-myopathy

References to Index of Diseases and Injuries

The code G71.3 has the following ICD-10-CM references to the Index of Diseases and Injuries

• Type 1 Excludes Notes:
  • Kearns-Sayre syndrome (@H49.81*)
  • Leber's disease (@H47.21*)
  • Leigh's encephalopathy (@G31.82*)
  • mitochondrial metabolism disorders (@E88.4*.-)
  • Reye's syndrome (@G93.7*)

Crosswalk Information

Similar Codes

This page was last updated on: 10/1/2023

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