Diagnosis Code

I42.0 DILATED CARDIOMYOPATHY


Code Information

Diagnosis Code: I42.0

Short Description: Dilated cardiomyopathy

Long Description: Dilated cardiomyopathy

The code I42.0 is VALID for claim submission

Code Classification:

  • Diseases of the circulatory system (I00–I99)
    • Other forms of heart disease (I30-I5A)
      • Cardiomyopathy (I42)
        • I42.0 Dilated cardiomyopathy

Code Version: 2022 ICD-10-CM


Synonyms

  • Autosomal dominant epidermolysis bullosa simplex
  • Autosomal recessive familial wooly hair
  • Cardiomyopathy caused by drug
  • Cardiomyopathy due to connective tissue disease
  • Cardiomyopathy due to mucopolysaccharidosis
  • Cardiomyopathy due to viral infection
  • Cardiomyopathy in Friedreich's ataxia
  • Cardiomyopathy in myotonic dystrophy
  • Cardiomyopathy with cataract and hip spine disease syndrome
  • Cardiovascular abnormality due to infective myocarditis
  • Cardiovascular abnormality due to infective myocarditis
  • Cardiovascular abnormality due to infective myocarditis
  • Cardiovascular abnormality due to infective myocarditis
  • Cardiovascular abnormality due to infective myocarditis
  • Congenital wooly hair
  • Congestive obstructive cardiomyopathy
  • Dilated cardiomyopathy
  • Dilated cardiomyopathy 3B
  • Dilated cardiomyopathy caused by anthracycline
  • Dilated cardiomyopathy due to amyloidosis
  • Dilated cardiomyopathy due to bacterial myocarditis
  • Dilated cardiomyopathy due to carnitine deficiency
  • Dilated cardiomyopathy due to dermatomyositis
  • Dilated cardiomyopathy due to electrolyte imbalance
  • Dilated cardiomyopathy due to familial storage disease
  • Dilated cardiomyopathy due to Friedreich's ataxia
  • Dilated cardiomyopathy due to fungal myocarditis
  • Dilated cardiomyopathy due to glycogen storage disease
  • Dilated cardiomyopathy due to granuloma
  • Dilated cardiomyopathy due to hemochromatosis
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infectious disease
  • Dilated cardiomyopathy due to infiltration
  • Dilated cardiomyopathy due to infiltration
  • Dilated cardiomyopathy due to infiltration
  • Dilated cardiomyopathy due to lysosomal storage disease
  • Dilated cardiomyopathy due to malignancy
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to metabolic disorder
  • Dilated cardiomyopathy due to mitochondrial disease
  • Dilated cardiomyopathy due to mucopolysaccharidosis
  • Dilated cardiomyopathy due to muscular dystrophy
  • Dilated cardiomyopathy due to muscular dystrophy
  • Dilated cardiomyopathy due to myotonic dystrophy
  • Dilated cardiomyopathy due to neuromuscular disorder
  • Dilated cardiomyopathy due to nutritional deficiency
  • Dilated cardiomyopathy due to nutritional deficiency
  • Dilated cardiomyopathy due to parasitic myocarditis
  • Dilated cardiomyopathy due to parasitic myocarditis
  • Dilated cardiomyopathy due to phytanic acid storage disease
  • Dilated cardiomyopathy due to polyarteritis nodosa
  • Dilated cardiomyopathy due to protozoan myocarditis
  • Dilated cardiomyopathy due to rheumatoid arthritis
  • Dilated cardiomyopathy due to sarcoidosis
  • Dilated cardiomyopathy due to systemic sclerosis
  • Dilated cardiomyopathy due to taurine deficiency
  • Dilated cardiomyopathy due to viral myocarditis
  • Dilated cardiomyopathy secondary to drug
  • Dilated cardiomyopathy secondary to radiation
  • Dilated cardiomyopathy with connective tissue disorder
  • Dilated cardiomyopathy with genetic marker
  • Dilated cardiomyopathy with hypergonadotropic hypogonadism syndrome
  • Erythrokeratodermia cardiomyopathy syndrome
  • Familial cardiomyopathy
  • Familial cardiomyopathy
  • Familial cardiomyopathy
  • Familial dilated cardiomyopathy with conduction defect due to LMNA mutation
  • Infiltrative cardiomyopathy
  • Infiltrative cardiomyopathy
  • Infiltrative cardiomyopathy
  • Intermediate epidermolysis bullosa simplex with cardiomyopathy
  • Ischemic congestive cardiomyopathy
  • Ischemic congestive cardiomyopathy
  • Ischemic dilated cardiomyopathy due to coronary artery disease
  • Microcephalus cardiomyopathy syndrome
  • Myocardial degeneration
  • Myocardial degeneration
  • Myocardial degeneration
  • Nonischemic congestive cardiomyopathy
  • Nonsenile cataract
  • Primary dilated cardiomyopathy
  • Primary familial dilated cardiomyopathy
  • Primary idiopathic dilated cardiomyopathy
  • Secondary dilated cardiomyopathy
  • Secondary nonischemic congestive cardiomyopathy
  • Sensorineural deafness with dilated cardiomyopathy syndrome
  • Wooly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome

Diagnostic Related Group(s)

The code I42.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Other Circulatory System Diagnoses With Mcc (314)
  • Other Circulatory System Diagnoses With Cc (315)
  • Other Circulatory System Diagnoses Without Cc/mcc (316)

References to Index of Diseases and Injuries

The code I42.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Congestive cardiomyopathy

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
I42.0 Right Arrow 425.4 Prim cardiomyopathy NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
I42 Cardiomyopathy
I42.1 Obstructive hypertrophic cardiomyopathy
I42.2 Other hypertrophic cardiomyopathy
I42.3 Endomyocardial (eosinophilic) disease
I42.4 Endocardial fibroelastosis
I42.5 Other restrictive cardiomyopathy
I42.6 Alcoholic cardiomyopathy
I42.7 Cardiomyopathy due to drug and external agent
I42.8 Other cardiomyopathies
I42.9 Cardiomyopathy, unspecified


This page was last updated on: 10/1/2023