Diagnosis Code

L40.1 GENERALIZED PUSTULAR PSORIASIS


Code Information

Diagnosis Code: L40.1

Short Description: Generalized pustular psoriasis

Long Description: Generalized pustular psoriasis

The code L40.1 is VALID for claim submission

Code Classification:

  • Diseases of the skin and subcutaneous tissue (L00–L99)
    • Papulosquamous disorders (L40-L45)
      • Psoriasis (L40)
        • L40.1 Generalized pustular psoriasis

Code Version: 2022 ICD-10-CM


Synonyms

  • Acute blistering eruption of skin
  • Acute blistering eruption of skin
  • Acute blistering eruption of skin
  • Acute blistering eruption of skin
  • Acute generalized pustular flare of preexisting plaque psoriasis
  • Acute generalized pustular psoriasis de novo
  • Circinate and annular pustular psoriasis
  • Exanthematous disorder
  • Generalized pustular psoriasis
  • Generalized pustular psoriasis
  • Generalized pustular psoriasis of pregnancy
  • Generalized pustular psoriasis, exanthematous type
  • Infantile pustular psoriasis
  • Localized pustular psoriasis
  • Plaque psoriasis
  • Plaque psoriasis with pustules
  • Pustular psoriasis

Diagnostic Related Group(s)

The code L40.1 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Minor Skin Disorders With Mcc (606)
  • Minor Skin Disorders Without Mcc (607)

References to Index of Diseases and Injuries

The code L40.1 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Impetigo herpetiformis
    • Von Zumbusch's disease

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
L40.1 Right Arrow 694.3 Impetigo herpetiformis
696.1 Other psoriasis

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
L40 Psoriasis
L40.0 Psoriasis vulgaris
L40.2 Acrodermatitis continua
L40.3 Pustulosis palmaris et plantaris
L40.4 Guttate psoriasis
L40.5 Arthropathic psoriasis
L40.50 Arthropathic psoriasis, unspecified
L40.51 Distal interphalangeal psoriatic arthropathy
L40.52 Psoriatic arthritis mutilans
L40.53 Psoriatic spondylitis
L40.54 Psoriatic juvenile arthropathy
L40.59 Other psoriatic arthropathy
L40.8 Other psoriasis
L40.9 Psoriasis, unspecified


This page was last updated on: 10/1/2023