Diagnosis Code

Q80.4 HARLEQUIN FETUS


Code Information

Diagnosis Code: Q80.4

Short Description: Harlequin fetus

Long Description: Harlequin fetus

The code Q80.4 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Congenital ichthyosis (Q80)
        • Q80.4 Harlequin fetus

Code Version: 2022 ICD-10-CM


Synonyms

  • Congenital ectropion
  • Congenital ectropion of lip
  • Harlequin change
  • Harlequin fetus
  • Harlequin ichthyosis
  • Harlequin syndrome
  • Segmental hyperhidrosis

Diagnostic Related Group(s)

The code Q80.4 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Minor Skin Disorders With Mcc (606)
  • Minor Skin Disorders Without Mcc (607)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q80.4 Right Arrow 757.1 Ichthyosis congenita

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q80 Congenital ichthyosis
Q80.0 Ichthyosis vulgaris
Q80.1 X-linked ichthyosis
Q80.2 Lamellar ichthyosis
Q80.3 Congenital bullous ichthyosiform erythroderma
Q80.8 Other congenital ichthyosis
Q80.9 Congenital ichthyosis, unspecified


This page was last updated on: 10/1/2023