Diagnosis Code

Q87.81 ALPORT SYNDROME


Code Information

Diagnosis Code: Q87.81

Short Description: Alport syndrome

Long Description: Alport syndrome

The code Q87.81 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Oth congenital malform syndromes affecting multiple systems (Q87)
        • Q87.81 Alport syndrome

Code Version: 2022 ICD-10-CM


Synonyms

  • Alport syndrome
  • Alport syndrome
  • Alport syndrome autosomal dominant
  • Alport syndrome autosomal recessive
  • Alport syndrome X-linked
  • Alport syndrome X-linked
  • Alport syndrome, intellectual disability, midface hypoplasia, elliptocytosis syndrome
  • Congenital nephritis
  • Congenital nephritis
  • Glomerular disease due to Alport syndrome
  • Hereditary elliptocytosis
  • X-linked diffuse leiomyomatosis with Alport syndrome
  • X-linked sensorineural hearing loss
  • X-linked sensorineural hearing loss

Diagnostic Related Group(s)

The code Q87.81 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Other Musculoskeletal System And Connective Tissue Diagnoses With Mcc (564)
  • Other Musculoskeletal System And Connective Tissue Diagnoses With Cc (565)
  • Other Musculoskeletal System And Connective Tissue Diagnoses Without Cc/mcc (566)

References to Index of Diseases and Injuries

The code Q87.81 has the following ICD-10-CM references to the Index of Diseases and Injuries

    Crosswalk Information

    ICD-10 Code ICD-9 Code ICD-9 Description
    Q87.81 Right Arrow 759.89 Specfied cong anomal NEC

    This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

    Similar Codes

    ICD-10 Code ICD-10 Description
    Q87 Other specified congenital malformation syndromes affecting multiple systems
    Q87.0 Congenital malformation syndromes predominantly affecting facial appearance
    Q87.1 Congenital malformation syndromes predominantly associated with short stature
    Q87.11 Prader-Willi syndrome
    Q87.19 Other congenital malformation syndromes predominantly associated with short stature
    Q87.2 Congenital malformation syndromes predominantly involving limbs
    Q87.3 Congenital malformation syndromes involving early overgrowth
    Q87.4 Marfan syndrome
    Q87.40 Marfan syndrome, unspecified
    Q87.41 Marfan syndrome with cardiovascular manifestations
    Q87.410 Marfan syndrome with aortic dilation
    Q87.418 Marfan syndrome with other cardiovascular manifestations
    Q87.42 Marfan syndrome with ocular manifestations
    Q87.43 Marfan syndrome with skeletal manifestation
    Q87.5 Other congenital malformation syndromes with other skeletal changes
    Q87.8 Other specified congenital malformation syndromes, not elsewhere classified
    Q87.82 Arterial tortuosity syndrome
    Q87.83 Bardet-Biedl syndrome
    Q87.84 Laurence-Moon syndrome
    Q87.85 MED13L syndrome
    Q87.89 Other specified congenital malformation syndromes, not elsewhere classified


    This page was last updated on: 10/1/2023