Diagnosis Code

K00.5 HEREDITARY DISTURBANCES IN TOOTH STRUCTURE, NEC


Code Information

Diagnosis Code: K00.5

Short Description: Hereditary disturbances in tooth structure, NEC

Long Description: Hereditary disturbances in tooth structure, not elsewhere classified

The code K00.5 is VALID for claim submission

Code Classification:

  • Diseases of the digestive system (K00–K95)
    • Diseases of oral cavity and salivary glands (K00-K14)
      • Disorders of tooth development and eruption (K00)
        • K00.5 Hereditary disturbances in tooth structure, NEC

Code Version: 2022 ICD-10-CM


Synonyms

  • Amelogenesis imperfecta
  • Amelogenesis imperfecta - hypomaturation - recessive pigmented
  • Amelogenesis imperfecta - hypomaturation - snow capped teeth
  • Amelogenesis imperfecta - hypoplastic autosomal dominant - local
  • Amelogenesis imperfecta - hypoplastic autosomal dominant - rough
  • Amelogenesis imperfecta - hypoplastic autosomal dominant - smooth
  • Amelogenesis imperfecta - recessive - rough
  • Amelogenesis imperfecta and gingival hyperplasia syndrome
  • Amelogenesis imperfecta co-occurrent with cone rod dystrophy
  • Amelogenesis imperfecta, hypocalcification type
  • Amelogenesis imperfecta, hypomaturation hypoplasia type with taurodontism
  • Amelogenesis imperfecta, hypomaturation type
  • Amelogenesis imperfecta, hypomaturation type
  • Amelogenesis imperfecta, hypoplastic type
  • Amelogenesis imperfecta, hypoplastic type
  • Amelogenesis imperfecta, hypoplastic type
  • Amelogenesis imperfecta, hypoplastic type with microdontia
  • Amelogenesis imperfecta, pigmented hypomaturation type
  • Atypical dentin dysplasia due to SMOC2 deficiency
  • Brachyolmia
  • Congenital anomaly of sclera
  • Deep occlusal groove
  • Dentin dysplasia
  • Dentin dysplasia
  • Dentin dysplasia with sclerotic bone syndrome
  • Dentin dysplasia, type I
  • Dentin dysplasia, type II
  • Dentinogenesis imperfecta
  • Dentinogenesis imperfecta
  • Dentinogenesis imperfecta
  • Dentinogenesis imperfecta
  • Dentinogenesis imperfecta
  • Dentinogenesis imperfecta - Shield's type I
  • Dentinogenesis imperfecta - Shield's type II
  • Dentinogenesis imperfecta - Shield's type III
  • Dentinogenesis imperfecta, short stature, hearing loss, intellectual disability syndrome
  • Dermo-odonto dysplasia
  • Enamel-renal syndrome
  • Goldblatt syndrome
  • Horner's teeth
  • Hyperplasia of gingiva
  • Hypocalcification of teeth
  • Hypomineralization of enamel of teeth
  • Hypomineralization of enamel of tooth
  • Hypomineralization of tooth
  • Microdontia
  • Nephrocalcinosis
  • Odontogenesis imperfecta
  • Osteogenesis imperfecta type I
  • Osteogenesis imperfecta with blue sclerae AND dentinogenesis imperfecta
  • Osteosclerosis
  • Shell teeth
  • Skeletal dysplasia with wormian bone, multiple fractures, dentinogenesis imperfecta syndrome
  • Taurodontism
  • Trichodysplasia with amelogenesis imperfecta syndrome
  • Verloes Bourguignon syndrome

References to Index of Diseases and Injuries

The code K00.5 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Amelogenesis imperfecta
    • Dentinogenesis imperfecta
    • Odontogenesis imperfecta
    • Dentinal dysplasia
    • Shell teeth

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
K00.5 Right Arrow 520.5 Heredit tooth struct NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
K00 Disorders of tooth development and eruption
K00.0 Anodontia
K00.1 Supernumerary teeth
K00.2 Abnormalities of size and form of teeth
K00.3 Mottled teeth
K00.4 Disturbances in tooth formation
K00.6 Disturbances in tooth eruption
K00.7 Teething syndrome
K00.8 Other disorders of tooth development
K00.9 Disorder of tooth development, unspecified


This page was last updated on: 10/1/2023