Diagnosis Code

Q04.3 OTHER REDUCTION DEFORMITIES OF BRAIN


Code Information

Diagnosis Code: Q04.3

Short Description: Other reduction deformities of brain

Long Description: Other reduction deformities of brain

The code Q04.3 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of the nervous system (Q00-Q07)
      • Other congenital malformations of brain (Q04)
        • Q04.3 Other reduction deformities of brain

Code Version: 2022 ICD-10-CM


Synonyms

  • Abnormality of neurogenesis
  • Abnormality of neurogenesis
  • Abnormality of neurogenesis
  • Absence of septum pellucidum
  • Agenesis of cerebellum
  • Agenesis of cerebellum
  • Agenesis of cerebellum
  • Agenesis of cerebrum
  • Agenesis of left hemisphere of cerebellum
  • Agenesis of right hemisphere of cerebellum
  • Aicardi's syndrome
  • Anomalies of hypothalamus
  • Anterior pituitary hormone deficiency
  • Aplasia of cerebellum
  • Aplasia of the vermis
  • Aprosencephaly
  • Aprosencephaly/atelencephaly spectrum
  • Arachnoid cyst
  • Atelencephaly
  • Autosomal recessive frontotemporal pachygyria
  • Bilateral frontal polymicrogyria
  • Bilateral frontoparietal polymicrogyria
  • Bilateral generalized polymicrogyria
  • Bilateral parasagittal parieto-occipital polymicrogyria
  • Bilateral polymicrogyria
  • Bilateral polymicrogyria
  • Cerebellum agenesis with hydrocephaly
  • Cerebral cortical dysgenesis
  • Cobblestone lissencephaly without muscular or ocular involvement
  • Combined malformation of central nervous system and skeletal muscle
  • Combined malformation of central nervous system and skeletal muscle
  • Complete agenesis of vermis
  • Congenital absence of part of brain
  • Congenital agenesis of brainstem nuclei
  • Congenital bilateral perisylvian syndrome
  • Congenital cerebellar hypoplasia
  • Congenital cerebellar hypoplasia co-occurrent with tapetoretinal degeneration
  • Congenital chorioretinal degeneration
  • Congenital conduction defect
  • Congenital diaphragmatic hernia
  • Congenital hepatic fibrosis
  • Congenital hypoplasia of cerebrum
  • Congenital hypoplasia of cerebrum
  • Congenital hypoplasia of inner granular layer of cerebellum
  • Congenital hypoplasia of part of brain
  • Congenital malformation of anterior pituitary
  • Congenital malformation of the meninges
  • Congenital muscular dystrophy with cerebellar involvement
  • Congenital pontocerebellar hypoplasia
  • Congenital pontocerebellar hypoplasia type 1
  • Congenital pontocerebellar hypoplasia type 10
  • Congenital pontocerebellar hypoplasia type 2
  • Congenital pontocerebellar hypoplasia type 3
  • Congenital pontocerebellar hypoplasia type 4
  • Congenital pontocerebellar hypoplasia type 5
  • Congenital pontocerebellar hypoplasia type 6
  • Congenital pontocerebellar hypoplasia type 7
  • Congenital pontocerebellar hypoplasia type 8
  • Congenital pontocerebellar hypoplasia type 9
  • Congenital porencephaly
  • Cortical dysgenesis with pontocerebellar hypoplasia due to TUBB3 mutation
  • Cortical dysplasia
  • Craniotelencephalic dysplasia
  • Dyke-Davidoff-Masson syndrome
  • Dysgenesis of the brainstem
  • Dysgenesis of the cerebellum
  • Early-onset progressive encephalopathy, hearing loss, pons hypoplasia, brain atrophy syndrome
  • Endosteal hyperostoses
  • Endosteal hyperostoses with cerebellar hypoplasia
  • Epileptic spasms
  • Familial aplasia of the vermis
  • Familial aplasia of the vermis
  • Familial aplasia of the vermis
  • Familial aplasia of the vermis
  • Familial aplasia of the vermis
  • Familial aplasia of the vermis
  • Familial aplasia of the vermis
  • Granular cell hypoplasia
  • Hemispheric cerebellar agenesis
  • Hemispheric cerebral agenesis
  • Hydranencephaly
  • Hydranencephaly
  • Hydranencephaly
  • Hydranencephaly
  • Hydranencephaly with proliferative vasculopathy
  • Hypoplasia of brain gyri
  • Intellectual disability, coarse face, macrocephaly, cerebellar hypotrophy syndrome
  • Isolated agenesis of cerebellar vermis
  • Isolated bilateral hemispheric cerebellar hypoplasia
  • Isolated cerebellar vermis hypoplasia
  • Isolated lissencephaly type 1 without known genetic defect
  • Isolated unilateral hemispheric cerebellar hypoplasia
  • Jeune thoracic dystrophy
  • Joubert syndrome
  • Joubert syndrome
  • Joubert syndrome
  • Joubert syndrome
  • Joubert syndrome
  • Joubert syndrome
  • Joubert syndrome
  • Joubert syndrome with congenital hepatic fibrosis
  • Joubert syndrome with Jeune asphyxiating thoracic dystrophy
  • Joubert syndrome with ocular defect
  • Joubert syndrome with oculorenal defect
  • Joubert syndrome with orofaciodigital defect
  • Joubert syndrome with renal defect
  • Lethal hydranencephaly, diaphragmatic hernia syndrome
  • Lissencephaly
  • Lissencephaly due to LIS1 mutation
  • Lissencephaly due to TUBA1A mutation
  • Lissencephaly syndrome Norman Roberts type
  • Lissencephaly type 1 due to doublecortin gene mutation
  • Lissencephaly type 3 familial fetal akinesia sequence syndrome
  • Lissencephaly type 3 metacarpal bone dysplasia syndrome
  • Lissencephaly with cerebellar hypoplasia
  • Lissencephaly with cerebellar hypoplasia type A
  • Lissencephaly with cerebellar hypoplasia type B
  • Lissencephaly with cerebellar hypoplasia type C
  • Lissencephaly with cerebellar hypoplasia type D
  • Lissencephaly with cerebellar hypoplasia type E
  • Lissencephaly with cerebellar hypoplasia type F
  • Macroencephaly
  • Macrogyria
  • Macrogyria
  • Macrogyria
  • MARCH syndrome
  • Megalencephaly, polymicrogyria, postaxial polydactyly, hydrocephalus syndrome
  • Microcephalus, cerebellar hypoplasia, cardiac conduction defect syndrome
  • Microcephaly, corpus callosum and cerebellar vermis hypoplasia, facial dysmorphism, intellectual disability syndrome
  • Microcephaly, polymicrogyria, corpus callosum agenesis syndrome
  • Microgyria
  • Microlissencephaly
  • Microlissencephaly
  • Microlissencephaly micromelia syndrome
  • Micromelia
  • NDE1-related microhydranencephaly
  • Neonatal diabetes mellitus
  • Nephronophthisis
  • Occipital pachygyria and polymicrogyria
  • Pachygyria, intellectual disability, epilepsy syndrome
  • Partial absence of septum pellucidum
  • Partial agenesis of corpus callosum
  • Partial corpus callosum agenesis, cerebellar vermis hypoplasia with posterior fossa cysts syndrome
  • Permanent neonatal diabetes mellitus
  • Permanent neonatal diabetes mellitus with cerebellar agenesis syndrome
  • Polymicrogyria due to TUBB2B mutation
  • Polymicrogyria with optic nerve hypoplasia
  • Pontine tegmental cap dysplasia
  • Porencephaly, cerebellar hypoplasia, internal malformations syndrome
  • Rhombencephalosynapsis
  • Short rib dysplasia
  • Short stature, pituitary and cerebellar defect and small sella turcica syndrome
  • Type 1 lissencephaly
  • Type 2 lissencephaly
  • Type 3 lissencephaly
  • Unilateral polymicrogyria
  • White matter hypoplasia, corpus callosum agenesis, intellectual disability syndrome
  • XK aprosencephaly syndrome
  • X-linked intellectual disability with cerebellar hypoplasia syndrome
  • X-linked intellectual disability, cerebellar hypoplasia, spondyloepiphyseal dysplasia syndrome
  • X-linked lissencephaly with abnormal genitalia syndrome

References to Index of Diseases and Injuries

The code Q04.3 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Absence of part of brain
    • Agenesis of part of brain
    • Agyria
    • Aplasia of part of brain
    • Hydranencephaly
    • Hypoplasia of part of brain
    • Lissencephaly
    • Microgyria
    • Pachygyria
  • Type 1 Excludes Notes:
    • congenital malformations of corpus callosum (@Q04.0*)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q04.3 Right Arrow 742.2 Reduction deform, brain

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q04 Other congenital malformations of brain
Q04.0 Congenital malformations of corpus callosum
Q04.1 Arhinencephaly
Q04.2 Holoprosencephaly
Q04.4 Septo-optic dysplasia of brain
Q04.5 Megalencephaly
Q04.6 Congenital cerebral cysts
Q04.8 Other specified congenital malformations of brain
Q04.9 Congenital malformation of brain, unspecified


This page was last updated on: 10/1/2023